Macular telangiectasia type II with pachychoroid spectrum of macular disorders

Purpose: To report the cases with features of macular telangiectasia type II and pachychoroid spectrum of macular disorders simultaneously. Methods: It is a retrospective case series from a tertiary eye care center. Multimodal imaging features of these eyes including color fundus photographs, red free imaging, short-wave autofluorescence, fundus fluorescein angiography, indocyanine green angiography, and optical coherence tomography were studied. Results: Six eyes of three patients having combination of macular telangiectasia type II and pachychoroid group of disorders were found. Three eyes showed features of central serous chorioretinopathy, one eye had polypoidal choroidal vasculopathy, one eye had pachychoroid pigment epitheliopathy and one had thickened choroid. Conclusion: This is the first report of macular telangiectasia type II in association with the pachychoroid spectrum of macular disorders and provides insight into possible common etiopathogenetic mechanisms.

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