We present the case of a 47-year-old woman with bilateral iridocorneal endothelial syndrome. The iridocorneal endothelial syndrome has heretofore been considered a unilateral disorder. However, a review of the literature and examination of the patient presented in this report indicate that bilateral occurrence of the iridocorneal endothelial syndrome is not uncommon. Consequently, it may be inappropriate to include unilaterality as a feature distinguishing the iridocorneal endothelial syndrome from similar conditions, most notably posterior polymorphous endothelial dystrophy.