Crossed testicular ectopia is a rare congenital malformation in which both testis are located in the same hemiscrotum, and is related to an anomaly in normal testicular descent. This entity was first described by Lenhossek in 1886 and posteriorly by Halstead in 1907. Since then, there have been described less than a hundred of cases of this rare congenital malformation. Several ethiopathogenic theories have been proposed, including testicular adherence to mullerian structures, fusion of the wolffian ducts or defective gubemacular development, although none of them has been widely accepted. Usually, clinical sign is an inguinal hernia with empty contralateral hemiscrotum, and sometimes both testis in ipsilateral hemiscrotum. A new case of this pathology is presented.