[Association of plastic bronchitis to protein-losing enteropathy after fontan operation].

We report an unusual case of association of plastic bronchitis (PB) to protein-losing enteropathy (PLE) in a girl of 4 years and 9 months of age with double inlet single left ventricle and ventriculoarterial concordance. submitted to total cavopulmonary surgery. with an intracardiac lateral tunnel at the age of three. The elimination of the 10 cm fibrin bronchial mold (PB) and the alpha-1-antitrypsin elevation of 52 mg/g in feces had both become outstanding. Using sildenafil. the thoracic duct ligature and the cardiac transplant were programmed in case of continuity of the process.

[1]  J. Tam,et al.  Resolution of protein-losing enteropathy with low-molecular weight heparin in an adult patient with Fontan palliation. , 2007, The Annals of thoracic surgery.

[2]  K. Cherian,et al.  Treatment of plastic bronchitis. , 2007, The Annals of thoracic surgery.

[3]  Hikoro Matsui,et al.  Pulmonary vasodilation therapy with sildenafil citrate in a patient with plastic bronchitis after the Fontan procedure for hypoplastic left heart syndrome. , 2006, The Journal of thoracic and cardiovascular surgery.

[4]  D. Drinkwater,et al.  Plastic bronchitis: is thoracic duct ligation a real surgical option? , 2006, The Annals of thoracic surgery.

[5]  L. Benson,et al.  Fenestration of the Fontan Circuit as Treatment for Plastic Bronchitis , 2005, Pediatric Cardiology.

[6]  S. Apostolopoulou,et al.  Bosentan induces clinical, exercise and hemodynamic improvement in a pre-transplant patient with plastic bronchitis after Fontan operation. , 2005, The Journal of heart and lung transplantation : the official publication of the International Society for Heart Transplantation.

[7]  R. Gibson,et al.  Plastic bronchitis in children: A case series and review of the medical literature , 2002, Pediatric pulmonology.

[8]  T. Graham.  Liver and Cardiac Function in the Long Term After Fontan Operation , 2009 .

[9]  K.,et al.  Plastic bronchitis in children with fontan palliation: Analogue to protein losing enteropathy? , 2001, Pediatric Cardiology.

[10]  J. Hess,et al.  Protein-losing enteropathy after Fontan operation. , 1984, The Journal of thoracic and cardiovascular surgery.