Beckwith-Wiedemann Syndrome

vus flammeus, and prominent eyes with infraorbital creases. Recognition of BWS is important because of the associated risk for development of embryonal neoplasms affecting abdominal organs, the need for prompt treatment of neonatal hypoglycemia, and for purposes of genetic counseling. The primary-care physician can provide a major source of support and reassurance for the family, from the initial informing diagnostic interview through the years of followup. It is important to emphasize that most infants with BWS grow up to become relatively normal adults.

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