Desmoplastic Infantil Ganglioglioma: A Case Report

Case Report Infantile GGDs are a group of rare neuroepithelial tumors that are benign to the small child, most often occurring in the first two years of life. In magnetic resonance imaging (MRI), it appears as a large supratentorial tumor with a double component: solid, with a broad base of dural; and central cystic implantation, whose wall, typically, does not improve after injection of the contrast product. Edema is usually absent, and when it exists, it is often unimportant with a low mass effect compared to tumor volume. The histological study finds a mixed cell population, with neuronal differentiation. Total resection, if possible, is the treatment of choice, and adjuvant treatment may not be necessary beyond surgery. Despite morphological and radiological similarity to aggressive tumors, GGDs have a good prognosis. We present an observation of a child with GGD and we review the anatomo-clinical, radiological and therapeutic characteristics of this group of very rare tumors.