Divided left atrium with obstruction of pulmonary venous return in the setting of hypoplasia of the left heart

We describe an infant with hypoplasia of the left heart diagnosed prenatally who, at birth, had signs of severe pulmonary venous obstruction. Echocardiography indicated normally connecting pulmonary veins, and showed a paradoxical right-to-left shunt across a patent oval foramen. Postmortem examination revealed that the obstruction was due to a divided left atrium, or cor triatriatum sinister, with an imperforate muscular diaphragm separating completely the two components of the divided atrium.

[1]  F. Cetta,et al.  Unusual finding of cor triatriatum in a newborn with hypoplastic left heart syndrome. , 2001, Journal of the American Society of Echocardiography : official publication of the American Society of Echocardiography.

[2]  J. Rychik,et al.  The hypoplastic left heart syndrome with intact atrial septum: atrial morphology, pulmonary vascular histopathology and outcome. , 1999, Journal of the American College of Cardiology.

[3]  J. Rychik,et al.  Long-term outcome of infants with single ventricle and total anomalous pulmonary venous connection. , 1999, The Journal of thoracic and cardiovascular surgery.

[4]  L. Gerlis,et al.  An unusual type of anomalous pulmonary venous drainage associated with a complex left heart hypoplasia and a variety of divided left atrium ("cor triatriatum"). , 1985, International journal of cardiology.

[5]  A. Starr,et al.  Common pulmonary vein atresia: Importance of immediate recognition and surgical intervention. , 1982, The Journal of thoracic and cardiovascular surgery.

[6]  F. Askin,et al.  Congenital alveolar capillary dysplasia--an unusual cause of respiratory distress in the newborn. , 1981, American journal of clinical pathology.

[7]  O. Thilenius,et al.  Subdivided left atrium: an expanded concept of cor triatriatum sinistrum. , 1976, The American journal of cardiology.

[8]  J. Edwards,et al.  Atresia of the common pulmonary vein. , 1962, Pediatrics.

[9]  W. Norwood,et al.  Patterns of anomalous pulmonary venous connection/drainage in hypoplastic left heart syndrome: diagnostic role of Doppler color flow mapping and surgical implications. , 1992, Journal of the American College of Cardiology.

[10]  J. Marín-García,et al.  Cor triatriatum: study of 20 cases. , 1975, The American journal of cardiology.