论文信息 - Isolated partial anomalous pulmonary venous return with intact atrial septum: a rare but treatable cause of pulmonary hypertension in adults.

Isolated partial anomalous pulmonary venous return with intact atrial septum: a rare but treatable cause of pulmonary hypertension in adults.

A 56-year-old woman presented with a 1-year history of progressive dyspnoea on exertion. Echocardiography and right heart catheterization demonstrated severe right ventricular enlargement and pulmonary hypertension (74/40 mmHg) without any evidence of atrial septal defect (ASD). Cardiac magnetic resonance (CMR) imaging was performed to identify possible causes. Cine MR showed severe right ventricular enlargement right ventricular end-diastolic volume index (RVEDVI) (160 mL/m2) with moderate systolic dysfunction right ventricular ejection fraction (RVEF) (35%) ( Panel …

A. Farzaneh-Far | S. Pauwaa

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