Velocardiofacial syndrome and DiGeorge sequence.

The VATER complex is a non-random combination of three or more vertebral, anorectal, tracheo-oesophageal, radial, and renal anomalies of unknown aetiology.' Cardiac abnormalities are sometimes also involved (VACTERL). It has not been recognised as a specific syndrome and its components are variable. Khoury et aP' in their population based study, emphasised the aetiological heterogeneity of this entity. Exposure to proges-

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