Aneurysm of the left subclavian artery associated with Turner's syndrome. Successful surgical treatment.

An unusual case of a 38-year-old woman with Turner's syndrome associated with aneurysmal dilation of the left subclavian artery is presented. Aortography revealed a fusiform aneurysm in the proximal segment of the left subclavian artery, which was as long as 6 cm. The diagnosis of Turner's syndrome was postoperatively confirmed by chromosomal study, which showed 45X0. The aneurysm was successfully removed and reconstruction was done by interposition of a woven Dacron graft, 8 mm in diameter and 6 cm in length, between the thoracic aorta and subclavian artery just proximal to the thoracic outlet. Microscopic findings of the resected tissue of the subclavian artery revealed deposition of acid mucopolysaccharide in the intima and media.