Role of epithelial HCO3⁻ transport in mucin secretion: lessons from cystic fibrosis.
暂无分享,去创建一个
[1] P. Quinton,et al. A new role for bicarbonate secretion in cervico‐uterine mucus release , 2010, The Journal of physiology.
[2] H. C. Hartzell,et al. Bestrophin-2 mediates bicarbonate transport by goblet cells in mouse colon. , 2010, The Journal of clinical investigation.
[3] C. Glass,et al. Pharmacological correction of a defect in PPARγ signaling ameliorates disease severity in Cftr-deficient mice , 2010, Nature Medicine.
[4] P. Quinton,et al. Normal mouse intestinal mucus release requires cystic fibrosis transmembrane regulator-dependent bicarbonate secretion. , 2009, The Journal of clinical investigation.
[5] A. Dėdinaitė,et al. Normal and friction forces between mucin and mucin-chitosan layers in absence and presence of SDS. , 2008, Journal of colloid and interface science.
[6] H. C. Hartzell,et al. Bestrophin Cl- channels are highly permeable to HCO3-. , 2008, American journal of physiology. Cell physiology.
[7] R. Boucher,et al. Evidence for airway surface dehydration as the initiating event in CF airway disease , 2007, Journal of internal medicine.
[8] P. Burgel,et al. A morphometric study of mucins and small airway plugging in cystic fibrosis , 2006, Thorax.
[9] A. Verkman,et al. Hyperacidity of secreted fluid from submucosal glands in early cystic fibrosis. , 2006, American journal of physiology. Cell physiology.
[10] J. Olsen,et al. pH-dependent Intraluminal Organization of Mucin Granules in Live Human Mucous/Goblet Cells* , 2005, Journal of Biological Chemistry.
[11] K. Barrett,et al. Heat-stable enterotoxin of Escherichia coli stimulates a non-CFTR-mediated duodenal bicarbonate secretory pathway. , 2005, American journal of physiology. Gastrointestinal and liver physiology.
[12] B. Rubin,et al. MUC5AC and MUC5B Mucins Are Decreased in Cystic Fibrosis Airway Secretions. , 2004, American journal of respiratory cell and molecular biology.
[13] Richard C Boucher,et al. Abnormal surface liquid pH regulation by cultured cystic fibrosis bronchial epithelium , 2003, Proceedings of the National Academy of Sciences of the United States of America.
[14] J. Filkowski,et al. Control of dynamic CFTR selectivity by glutamate and ATP in epithelial cells , 2003, Nature.
[15] E. Larsen. Hans H. Ussing--scientific work: contemporary significance and perspectives. , 2002, Biochimica et biophysica acta.
[16] I. Gipson. Mucins of the human endocervix. , 2001, Frontiers in bioscience : a journal and virtual library.
[17] K. Kunzelmann,et al. CFTR: interacting with everything? , 2001, News in physiological sciences : an international journal of physiology produced jointly by the International Union of Physiological Sciences and the American Physiological Society.
[18] A. Cuthbert. Bicarbonate secretion in the murine gallbladder--lessons for the treatment of cystic fibrosis. , 2001, JOP : Journal of the pancreas.
[19] J. Kaunitz,et al. Dynamic regulation of mucus gel thickness in rat duodenum. , 2000, American journal of physiology. Gastrointestinal and liver physiology.
[20] S. Randell,et al. Evidence for Periciliary Liquid Layer Depletion, Not Abnormal Ion Composition, in the Pathogenesis of Cystic Fibrosis Airways Disease , 1998, Cell.
[21] J. Pearson,et al. The MUC2 gene product: a human intestinal mucin. , 1998, The international journal of biochemistry & cell biology.
[22] D. Benos,et al. Cystic fibrosis: a multiple exocrinopathy caused by dysfunctions in a multifunctional transport protein. , 1998, The American journal of medicine.
[23] L. Clarke,et al. Dual role of CFTR in cAMP-stimulated[Formula: see text] secretion across murine duodenum. , 1998, American journal of physiology. Gastrointestinal and liver physiology.
[24] K. Ossenkopp,et al. Taste reactivity responses in rats: influence of sex and the estrous cycle. , 1998, American journal of physiology. Regulatory, integrative and comparative physiology.
[25] H. Rossmann,et al. A functional CFTR protein is required for mouse intestinal cAMP‐, cGMP‐ and Ca2+‐dependent HCO3− secretion , 1997, The Journal of physiology.
[26] M. Gray,et al. cAMP-regulated whole cell chloride currents in pancreatic duct cells. , 1993, The American journal of physiology.
[27] M. Welsh,et al. cAMP stimulates bicarbonate secretion across normal, but not cystic fibrosis airway epithelia. , 1992, The Journal of clinical investigation.
[28] P. Quinton. Cystic fibrosis: a disease in electrolyte transport , 1990, FASEB journal : official publication of the Federation of American Societies for Experimental Biology.
[29] L. Tsui,et al. Identification of the cystic fibrosis gene: genetic analysis. , 1989, Science.
[30] L. Tsui,et al. Identification of the cystic fibrosis gene: cloning and characterization of complementary DNA. , 1989, Science.
[31] M. Corey,et al. Impaired chloride secretion, as well as bicarbonate secretion, underlies the fluid secretory defect in the cystic fibrosis pancreas. , 1988, Gastroenterology.
[32] P. Quinton,et al. Permeability properties of cell membranes and tight junctions of normal and cystic fibrosis sweat ducts , 1987, Pflügers Archiv.
[33] P. Verdugo,et al. Molecular Mechanism of Mucin Secretion: I. The Role of Intragranular Charge Shielding , 1987, Journal of dental research.
[34] P. Quinton,et al. Influence of abnormal Cl- impermeability on sweating in cystic fibrosis. , 1984, The American journal of physiology.
[35] K. Sato,et al. Defective beta adrenergic response of cystic fibrosis sweat glands in vivo and in vitro. , 1984, The Journal of clinical investigation.
[36] M. Knowles,et al. Abnormal ion permeation through cystic fibrosis respiratory epithelium. , 1983, Science.
[37] P. Quinton,et al. Higher bioelectric potentials due to decreased chloride absorption in the sweat glands of patients with cystic fibrosis. , 1983, The New England journal of medicine.
[38] P. Quinton,et al. Chloride impermeability in cystic fibrosis , 1983, Nature.
[39] M. Corey,et al. Evidence for a Primary Defect of Pancreatic HCO3− Secretion in Cystic Fibrosis , 1982, Pediatric Research.
[40] M. Knowles,et al. Increased bioelectric potential difference across respiratory epithelia in cystic fibrosis. , 1981, The New England journal of medicine.
[41] H. Shwachman,et al. Water and electrolytes in cervical mucus from patients with cystic fibrosis. , 1973, Fertility and sterility.
[42] G. Harrison,et al. Structure and ultrastructure of the labial salivary glands in patients with cystic fibrosis , 1971, Journal of clinical pathology.
[43] F. S. Nakayaam. CALCIUM ACTIVITY, COMPLEX AND ION‐PAIR IN SATURATED CaCO3 , 1968 .
[44] H. Shwachman,et al. Reproductive failure in males with cystic fibrosis. , 1968, The New England journal of medicine.
[45] C. Anderson,et al. PANCREOZYMIN ‐ SECRETIN TEST OF EXOCRINE PANCREATIC FUNCTION IN CYSTIC FIBROSIS AND THE SIGNIFICANCE OF THE RESULT FOR THE PATHOGENESIS OF THE DISEASE * , 1968, Canadian Medical Association journal.
[46] P. di Sant'Agnese,et al. Sweat electrolyte disturbances associated with childhood pancreatic disease. , 1953, The American journal of medicine.
[47] P. di Sant'Agnese,et al. Abnormal electrolyte composition of sweat in cystic fibrosis of the pancreas; clinical significance and relationship to the disease. , 1953, Pediatrics.
[48] H H USSING,et al. Active transport of sodium as the source of electric current in the short-circuited isolated frog skin. , 1951, Acta physiologica Scandinavica.
[49] W. Zuelzer,et al. The pathogenesis of fibrocystic disease of the pancreas; a study of 36 cases with special reference to the pulmonary lesions. , 1949, Pediatrics.
[50] D. Andersen. CYSTIC FIBROSIS OF THE PANCREAS AND ITS RELATION TO CELIAC DISEASE: A CLINICAL AND PATHOLOGIC STUDY , 1938 .
[51] P. Quinton. Birth of mucus. , 2010, American journal of physiology. Lung cellular and molecular physiology.
[52] J. Griffith,et al. Unpacking a gel-forming mucin: a view of MUC5B organization after granular release. , 2010, American journal of physiology. Lung cellular and molecular physiology.
[53] J. Riordan,et al. Identification of the Cystic Fibrosis Gene : Chromosome Walking and Jumping Author ( s ) : , 2008 .
[54] P. Quinton. Physiological basis of cystic fibrosis: a historical perspective. , 1999, Physiological reviews.
[55] G. Nicaise,et al. The calcium loading of secretory granules. A possible key event in stimulus‐secretion coupling , 1992, Biology of the cell.
[56] G. Szeifert,et al. Pathological confirmation of foetal cystic fibrosis following prenatal diagnosis. , 1990, Acta morphologica Hungarica.
[57] P. Verdugo,et al. Donnan mechanism of mucin release and conditioning in goblet cells: the role of polyions. , 1989, Symposia of the Society for Experimental Biology.
[58] J. F. Kelly,et al. The pathogenesis of fibrocystic disease of the pancreas. , 1953, Bulletin. Georgetown University. Medical Center.