Bilateral Presentation of Pleural Desmoplastic Small Round Cell Tumors: A Case Report

Desmoplastic small round cell tumor (DSRCT) is a highly aggressive malignant small cell neoplasm that tends to affect adolescents and young adults and occurs predominantly in the abdominal cavity, including the pelvis and omentum (1, 2). Other primary sites are rare and have included the paratesticular region, pleura, posterior cranial fossa, soft tissues, bone, ovary, and kidney (2-4). DSRCT in the lung is extremely rare. This distinct clinicopathological entity was first described by Gerald and Rosai (1) in 1989. A DSRCT is composed of small round tumor cells of uncertain histogenesis, associated with prominent stromal desmoplasia and polyphenotypic differentiation. This article reports bilateral tumors in the pleura of a 15-year-old male. CASE REPORT

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