Intraventricular chordoid meningioma in a child: fever of unknown origin, clinical course, and response to treatment.

The authors present the case of an 11-year-old boy with an intraventricular chordoid meningioma, which is a rare presentation of prolonged fever of unknown origin due to a rare tumor in a rare location. The fever resolved after excision of the lesion. Subsequent imaging revealed recurrence at 1 year. After a repeat excision and fractionated radiotherapy, the patient has remained disease free 5 years after the first surgery. Very few cases of intraventricular chordoid meningioma have been reported to date. The pathological features and clinical course are described. A review of the literature describing management options for this tumor type, recently found to have a higher recurrence rate, is described herein.

[1]  H. Kinouchi,et al.  Clear cell meningioma causing Castleman syndrome in a child. , 2010, Journal of neurosurgery. Pediatrics.

[2]  T. Gupta,et al.  A primary optic nerve sheath chordoid meningioma , 2010, Journal of Clinical Neuroscience.

[3]  K. Wang,et al.  Third ventricular chordoid meningioma in a child. , 2008, Journal of neurosurgery. Pediatrics.

[4]  H. McDowell,et al.  Malignant disseminated chordoid meningioma in a 12-year-old child: a role for early cranial and spinal radiation treatment after subtotal resection , 2006, Child's Nervous System.

[5]  L. Ferrante,et al.  Intracranial Meningiomas in Children: Report of 27 New Cases and Critical Analysis of 440 Cases Reported in the Literature , 2006, Journal of child neurology.

[6]  I. Perrotta,et al.  Chordoid Meningioma: Case Report and Literature Review , 2006, Ultrastructural pathology.

[7]  R. Pallini,et al.  Pyrogenic cytokine interleukin-6 expression by a chordoid meningioma in an adult with a systemic inflammatory syndrome. Case report and review of the literature. , 2005, Journal of neurosurgery.

[8]  P. Gutin,et al.  Diagnosis and Treatment of Atypical and Anaplastic Meningiomas: A Review , 2005, Neurosurgery.

[9]  J. Yoshida,et al.  Intraventricular chordoid meningioma presenting with Castleman disease due to overproduction of interleukin-6. Case report. , 2005, Journal of neurosurgery.

[10]  J. Szelényi.  Cytokines and the central nervous system , 2001, Brain Research Bulletin.

[11]  B. Scheithauer,et al.  Chordoid meningioma: a clinicopathologic study of 42 cases. , 2000, The American journal of surgical pathology.

[12]  H. Ito,et al.  Chordoid meningioma in a child. Case report. , 1998, Journal of neurosurgery.

[13]  L. Taillandier,et al.  [Chordoid meningiomas. Clinical, neuroradiological and anatomopathological aspects. Apropos of a new case and review of the literature]. , 1997, Neuro-Chirurgie.

[14]  F. Vogel,et al.  “Chordoid” meningeal tumors in young individuals with peritumoral lymphoplasmacellular infiltrates causing systemic manifestations of the castleman syndrome. A report of seven cases , 1988, Cancer.