Primitive Neuroectodermal Tumor of the Pancreas: A Case Report and Review of the Literature

Primitive neuroectodermal tumors (PNETs) are presented as rare malignant neoplasms. In unusual cases, those neoplasms may arise in solid organs containing neuroendocrine cells, such as the pancreas. Herein the case of a 28-year-old patient that underwent gastroduodenopancreatectomy after the diagnosis of a huge mass (PNET) located in both head and body of the pancreas is reported. This is the 19th case of pancreatic PNET reported in literature.

[1]  Aaas News,et al.  Book Reviews , 1893, Buffalo Medical and Surgical Journal.

[2]  Song-Cheol Kim,et al.  Primary Mesenchymal Tumors of the Pancreas: Single-Center Experience Over 16 Years , 2014, Pancreas.

[3]  I. Cecconello,et al.  [Pancreatic primitive neuroectodermal tumor: case report]. , 2013, Arquivos brasileiros de cirurgia digestiva : ABCD = Brazilian archives of digestive surgery.

[4]  S. Du,et al.  Peripheral primitive neuroectodermal tumors arising in the pancreas: the first case report in Asia and a review of the 14 total reported cases in the world. , 2013, Hepatobiliary surgery and nutrition.

[5]  I. Cecconello,et al.  TUMOR PRIMITIVO ECTODÉRMICO PANCREÁTICO: RELATO DE CASO Pancreatic primitive neuroectodermal tumor: case report , 2013 .

[6]  W. Marsden.  I and J , 2012 .

[7]  E. Gillies,et al.  Extraosseous Ewing’s sarcoma of the pancreas , 2012, International Journal of Clinical Oncology.

[8]  M. Nowicki,et al.  Uncommon presentation of rare disorder-duodenal ulcer secondary to invasive pancreatic primitive neuroectodermal tumor: case report and review of the literature. , 2011, Journal of pediatric hematology/oncology.

[9]  Naomi J Balamuth,et al.  Ewing's sarcoma. , 2010, The Lancet. Oncology.

[10]  H. Atkinson,et al.  Perigastric extraskeletal Ewing's sarcoma: a case report. , 2009, World journal of gastroenterology.

[11]  Warren P Schutte,et al.  Precocious puberty because of a pancreatic neuroectodermal tumor. , 2006, Journal of pediatric surgery.

[12]  P. Kienle,et al.  Huge primitive neuroectodermal tumor of the pancreas: report of a case and review of the literature. , 2006, World journal of gastroenterology.

[13]  Wei-hua Wu,et al.  [Primitive neuroectodermal tumor of pancreas]. , 2006, Zhonghua bing li xue za zhi = Chinese journal of pathology.

[14]  F. Tzortzatou-Stathopoulou,et al.  Favorable outcome of Ewing sarcoma family tumors to multiagent intensive preoperative chemotherapy: A single institution experience , 2005, Journal of surgical oncology.

[15]  A. Perek,et al.  Primitive Neuroectodermal Tumor of the Pancreas , 2003, Pancreatology.

[16]  A. Perek,et al.  Primitive neuroectodermal tumor of the pancreas. A case report of an extremely rare tumor. , 2003, Pancreatology : official journal of the International Association of Pancreatology (IAP) ... [et al.].

[17]  R. Hruban,et al.  Primitive Neuroectodermal Tumors of the Pancreas: A Report of Seven Cases of a Rare Neoplasm , 2002, The American journal of surgical pathology.

[18]  Kevin Barraclough,et al.  I and i , 2001, BMJ : British Medical Journal.

[19]  I. Joppich,et al.  Primitive Neuroectodermal Tumor of the Pancreas An Extremely Rare Tumor , 2000, Klinische Padiatrie.

[20]  M. Ladanyi,et al.  Contribution of molecular genetic data to the classification of sarcomas. , 2000, Human pathology.

[21]  W. Gerald,et al.  Molecular biology of the Ewing's sarcoma/primitive neuroectodermal tumor family. , 2000, Journal of clinical oncology : official journal of the American Society of Clinical Oncology.

[22]  B. Rougraff,et al.  Extraskeletal Ewing's sarcoma , 1999, Cancer.

[23]  H. Grier.  The Ewing family of tumors. Ewing's sarcoma and primitive neuroectodermal tumors. , 1997, Pediatric clinics of North America.

[24]  J. Kußmann,et al.  Maligne nichtepitheliale Tumoren des Pankreas , 1997, Der Pathologe.

[25]  G. Zamboni,et al.  [Malignant non-epithelial tumors of the pancreas]. , 1997, Der Pathologe.

[26]  N. Weidner,et al.  Immunohistochemical Profile of Monoclonal Antibody 013: Antibody That Recognizes Glycoprotein p30/32MIC2 and is Useful in Diagnosing Ewing's Sarcoma and Peripheral Neuroepithelioma , 1994, The American journal of surgical pathology.

[27]  N. D. Reis,et al.  [Extraskeletal Ewing's sarcoma]. , 1984, Harefuah.

[28]  T. Nakajima,et al.  Malignant neuroepithelioma (peripheral neuroblastoma): A clinicopathologic study of 15 cases , 1983, The American journal of surgical pathology.

[29]  A. Cabrera,et al.  EWING'S SARCOMA. , 1964, Surgery, gynecology & obstetrics.