Rapunzel Syndrome Reviewed and Redefined

Rapunzel syndrome is a rare presentation of a trichobezoar, with 24 cases having been reported in literature so far. This syndrome has been reported in 23 female and 1 male patient with a mean age of 10.8 years. The patients commonly present with abdominal pain, nausea, vomiting and signs of obstruction. The distal end of the bezoar may be in the jejunum, ileum or the colon. We evaluate the various cases reported and discuss the various modes of presentation of this uncommon syndrome, and also present a series of 3 cases, all females, aged 16, 18 and 21 years, and had a trichobezoar in the stomach with a tail extending into the ileum.

[1]  M. Pul,et al.  The rapunzel syndrome (trichobezoar) causing gastric perforation in a child: A case report , 2005, European Journal of Pediatrics.

[2]  D. Chelly,et al.  The Rapunzel syndrome: case report and review of the literature , 1996, Pediatric Surgery International.

[3]  P. Mandhan,et al.  Recurrent Rapunzel syndrome - a case report. , 2003, Medical science monitor : international medical journal of experimental and clinical research.

[4]  D. Lorenz,et al.  [The Rapunzel syndrome: rare manifestation of a trichobezoar of the upper gastrointestinal tract]. , 2003, Der Chirurg; Zeitschrift fur alle Gebiete der operativen Medizen.

[5]  D. Lorenz,et al.  Das Rapunzel-Syndrom , 2003, Der Chirurg.

[6]  M. Schein,et al.  Rapunzel syndrome causing gastric emphysema and small bowel obstruction. , 2003, Surgery.

[7]  A. Pace,et al.  Trichobezoar in a 13 year old Male: a case report and review of literature , 2003 .

[8]  Curioso Vilchez Wh,et al.  [Rapunzel syndrome: case report and literature review]. , 2002 .

[9]  Walter H Curioso Vilchez,et al.  [Rapunzel syndrome: case report and literature review]. , 2002, Revista de gastroenterologia del Peru : organo oficial de la Sociedad de Gastroenterologia del Peru.

[10]  R. Couper.  Rapunzel syndrome , 2001, The Lancet.

[11]  A. Deshpande,et al.  Rapunzel syndrome with a long tail , 2001, Indian journal of pediatrics.

[12]  S. Avilla,et al.  [The Rapunzel syndrome - a case report: trichobezoar as a cause of intestinal perforation] , 2000, Jornal de pediatria.

[13]  K. Deeg,et al.  [Rapunzel syndrome, an rare form of intestinal trichobezoars]. , 1999, Klinische Padiatrie.

[14]  S. Pandit,et al.  Rapunzel syndrome—a case report , 1999, American Journal of Gastroenterology.

[15]  S. Wainer,et al.  The Rapunzel syndrome (trichobezoar) causing atypical intussusception in a child: a case report. , 1999, Journal of pediatric surgery.

[16]  G. Drugas,et al.  Gastric trichobezoar: case report and literature review. , 1998, Mayo Clinic proceedings.

[17]  O. Dilek,et al.  Trichobezoars as a cause of gastrointestinal obstructions: the Rapunzel syndrome. , 1996, Acta gastro-enterologica Belgica.

[18]  J. UrozTristán,et al.  [Rapunzel syndrome: a report of a new case]. , 1996 .

[19]  J. Torralba,et al.  Gastrointestinal bezoars , 1994, The British journal of surgery.

[20]  N. Duncan,et al.  The Rapunzel syndrome. Report of a case and review of the literature. , 1994, The West Indian medical journal.

[21]  M. Demircan,et al.  The Rapunzel Syndrome: A Case Report and Review of the Literature , 1993, European journal of pediatric surgery : official journal of Austrian Association of Pediatric Surgery ... [et al] = Zeitschrift fur Kinderchirurgie.

[22]  V. Sharma,et al.  Gastro-intestinal bezoars. , 1991, Journal of the Indian Medical Association.

[23]  K. Panesar,et al.  The Rapunzel syndrome: a rare presentation of trichobezoar. , 1989, The Ulster medical journal.

[24]  Wolfson Pj,et al.  The Rapunzel syndrome: an unusual trichobezoar. , 1987 .

[25]  R. J. Fabius,et al.  The Rapunzel syndrome: an unusual trichobezoar. , 1987, American Journal of Gastroenterology.

[26]  M. Praet,et al.  An unusual case of the trichobezoar: the Rapunzel syndrome. , 1982, American Journal of Gastroenterology.

[27]  L. Teodori,et al.  Report of a Case and Review of the Literature , 1981 .

[28]  Willard A. Burns,et al.  Report of a Case and Review of the Literature , 2017 .

[29]  E. Vaughan,et al.  The Rapunzel syndrome. An unusual complication of intestinal bezoar. , 1968, Surgery.