Reduced cholesterol accumulation and improved deficient peroxisomal functions in a murine model of Niemann-Pick type C disease upon treatment with peroxisomal proliferators.
暂无分享,去创建一个
[1] T. Singer. Determination of the activity of succinate, NADH, choline, and alpha-glycerophosphate dehydrogenases. , 2006, Methods of biochemical analysis.
[2] W. Pavan,et al. Murine model of Niemann-Pick C disease: mutation in a cholesterol homeostasis gene. , 1997, Science.
[3] K. G. Coleman,et al. Niemann-Pick C1 disease gene: homology to mediators of cholesterol homeostasis. , 1997, Science.
[4] G. Dallner,et al. Peroxisomal Impairment in Niemann-Pick Type C Disease* , 1997, The Journal of Biological Chemistry.
[5] G. Dallner,et al. Changes in the Levels of Dolichol and Dolichyl Phosphate in a Murine Model of Niemann‐Pick's Type C Disease , 1995, Journal of neurochemistry.
[6] H. Mandel,et al. Reduced cellular cholesterol content in peroxisome-deficient fibroblasts is associated with impaired uptake of the patient's low density lipoprotein and with reduced cholesterol synthesis. , 1995, Journal of lipid research.
[7] J. Ericsson,et al. Isoprenoid biosynthesis in rat liver peroxisomes. Characterization of cis-prenyltransferase and squalene synthetase. , 1992, The Journal of biological chemistry.
[8] R. Brady,et al. Deficiencies in sex-regulated expression and levels of two hepatic sterol carrier proteins in a murine model of Niemann-Pick type C disease. , 1992, Journal of Biological Chemistry.
[9] I. Issemann,et al. Activation of a member of the steroid hormone receptor superfamily by peroxisome proliferators , 1990, Nature.
[10] G. Dallner,et al. Compartmentalization of phosphatidylethanolamine in microsomal membranes from rat liver. , 1982, Journal of lipid research.
[11] D. Glick. Methods of Biochemical Analysis , 1968 .
[12] Oliver H. Lowry,et al. Protein measurement with the Folin phenol reagent. , 1951, The Journal of biological chemistry.
[13] L. Liscum,et al. Biological implications of the Niemann-Pick C mutation. , 1997, Sub-cellular biochemistry.