Expression of lamin A mutated in the carboxyl-terminal tail generates an aberrant nuclear phenotype similar to that observed in cells from patients with Dunnigan-type partial lipodystrophy and Emery-Dreifuss muscular dystrophy.
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C. Vigouroux | B. Buendia | J. Capeau | H. Worman | J. Courvalin | C. Ostlund | E. Dubosclard | M. Wehnert | C. Favreau | D. Higuet