Teratoid Medulloepithelioma: A Rare Intraocular Tumor of a Child

Medulloepithelioma is a rare congenital neuroepithelial tumor commonly arising from the non-pigmented ciliary body epithelium and rarely from iris, retina or the optic nerve. It occurs in patient under 10 years. It is a rare neuroepithelial tumor and is the second most frequent intraocular tumour in children after retinoblastoma. Unlike cases reported in the literature in which the tumour recurs rapidly, recurrence occurred in our case five years later.

[1]  C. Shields,et al.  Ciliary body medulloepithelioma association with pleuropulmonary blastoma in a familial tumor predisposition syndrome. , 2014, Journal of pediatric ophthalmology and strabismus.

[2]  C. Margo,et al.  Intraocular medulloepithelioma. , 2012, Archives of pathology & laboratory medicine.

[3]  Gretchen M. Williams,et al.  Ciliary body medulloepithelioma: four cases associated with pleuropulmonary blastoma—a report from the International Pleuropulmonary Blastoma Registry , 2010, British Journal of Ophthalmology.

[4]  M. O'hara,et al.  Malignant teratoid medulloepithelioma: clinical-echographic-histopathologic correlation. , 2001, Journal of AAPOS : the official publication of the American Association for Pediatric Ophthalmology and Strabismus.

[5]  F. Stefani,et al.  Medulloepithelioma of the ciliary body , 1991, Acta ophthalmologica.

[6]  A. Panda,et al.  Medulloepithelioma of the ciliary body. , 1985, Indian journal of ophthalmology.

[7]  L. Yanko,et al.  Teratoid intraocular medulloepithelioma. , 1978, American journal of ophthalmology.

[8]  W. Green,et al.  Malignant teratoid medulloepithelioma of the optic nerve. , 1974, Archives of ophthalmology.

[9]  J. Mullaney Primary malignant medulloepithelioma of the retinal stalk. , 1974, American journal of ophthalmology.

[10]  S. R. Andersen Differentiation features in some retinal tumors and in dysplastic retinal conditions. , 1971, American journal of ophthalmology.

[11]  S. R. Andersen MEDULLOEPITHELIOMA OF THE RETINA , 1962 .

[12]  A. B. Reese Medulio-epithelioma (dictyoma) of the optic nerve. , 1957, American journal of ophthalmology.