A Child with PFAPA Syndrome Complicated by Pityriasis Lichenoides et Varioliformis Acuta

Abstract:  We encountered a boy with periodic fever, aphthous‐stomatitis, pharyngitis, adenitis syndrome, complicated by a papular rash representing pityriasis lichenoides et varioliformis acuta. Proinflammatory cytokines have been implicated in both diseases and may represent the underlying common immunologic mechanism causing the two diseases.