Local bulging of the skull and external hydrocephalus due to cerebral agenesis.

Five cases are described and reference is made to two previously reported cases where there was bulging of the temporal region of the head. Radiographs of the skull showed that the temporal squama was bulged outwards and the lesser and greater wings of the sphenoid protruded forwards and upwards. Air studies and arteriograms showed a typical pattern. Surgery was not indicated except for the complication of an intracranial haematoma. The literature is reviewed, and an entity of local skull bulging with an external hydrocephalus due to agenesis of the temporal lobe of the brain and its complication of blood clot formation is defined. The relation of this syndrome to that of juvenile relapsing subdural haematoma is discussed.