Consequences of the combined deficiency in dystrophin and utrophin on the mechanical properties and myosin composition of some limb and respiratory muscles of the mouse

[1]  K. Davies,et al.  Expression of truncated utrophin leads to major functional improvements in dystrophin-deficient muscles of mice , 1997, Nature Medicine.

[2]  Susan C. Brown,et al.  Utrophin-Dystrophin-Deficient Mice as a Model for Duchenne Muscular Dystrophy , 1997, Cell.

[3]  J. Sanes,et al.  Skeletal and Cardiac Myopathies in Mice Lacking Utrophin and Dystrophin: A Model for Duchenne Muscular Dystrophy , 1997, Cell.

[4]  K. Davies,et al.  Postsynaptic Abnormalities at the Neuromuscular Junctions of Utrophin-deficient Mice , 1997, The Journal of cell biology.

[5]  J. Sanes,et al.  Subtle Neuromuscular Defects in Utrophin-deficient Mice , 1997, The Journal of cell biology.

[6]  K. Davies,et al.  Amelioration of the dystrophic phenotype of mdx mice using a truncated utrophin transgene , 1996, Nature.

[7]  G. Maréchal,et al.  Isoforms of myosin in growing muscles of ky (kyphoscoliotic) mice. , 1996, European journal of biochemistry.

[8]  J. Gillis,et al.  The mdx mouse: why diaphragm? , 1996, Muscle & nerve.

[9]  M. Perricaudet,et al.  Functional protection of dystrophic mouse (mdx) muscles after adenovirus-mediated transfer of a dystrophin minigene. , 1996, Proceedings of the National Academy of Sciences of the United States of America.

[10]  C. Reggiani,et al.  Molecular diversity of myofibrillar proteins: gene regulation and functional significance. , 1996, Physiological reviews.

[11]  G. Maréchal,et al.  Mechanical power and myosin composition of soleus and extensor digitorum longus muscles of ky mice. , 1995, The American journal of physiology.

[12]  C. Reggiani,et al.  Myosin isoforms in mammalian skeletal muscle. , 1994, Journal of applied physiology.

[13]  H. Sweeney,et al.  Adaptations in myosin heavy chain expression and contractile function in dystrophic mouse diaphragm. , 1993, The American journal of physiology.

[14]  H. Sweeney,et al.  Dystrophin protects the sarcolemma from stresses developed during muscle contraction. , 1993, Proceedings of the National Academy of Sciences of the United States of America.

[15]  K. Davies,et al.  Primary structure of dystrophin-related protein , 1992, Nature.

[16]  G. Vrbóva,et al.  Adaptation of mammalian skeletal muscle fibers to chronic electrical stimulation. , 1992, Reviews of physiology, biochemistry and pharmacology.

[17]  Simon C Watkins,et al.  Immunolocalization and developmental expression of dystrophin related protein in skeletal muscle , 1991, Neuromuscular Disorders.

[18]  J. Shrager,et al.  The mdx mouse diaphragm reproduces the degenerative changes of Duchenne muscular dystrophy , 1991, Nature.

[19]  H. Westerblad,et al.  Force decline due to fatigue and intracellular acidification in isolated fibres from mouse skeletal muscle. , 1991, The Journal of physiology.

[20]  C. Carlson,et al.  A noninvasive procedure to detect muscle weakness in the mdx mouse , 1990, Muscle & nerve.

[21]  F. Pons,et al.  Présence d'une protéine de type dystrophine au niveau de la jonction neuromusculaire dan sla dystrophie musculaire de Duchenne et la souris mutante mdx , 1990 .

[22]  D. Pette,et al.  Cellular and molecular diversities of mammalian skeletal muscle fibers. , 1990, Reviews of physiology, biochemistry and pharmacology.

[23]  E A Barnard,et al.  The molecular basis of muscular dystrophy in the mdx mouse: a point mutation. , 1989, Science.

[24]  N. Curtin,et al.  THE mdx MOUSE SKELETAL MUSCLE MYOPATHY: II. CONTRACTILE PROPERTIES , 1988, Neuropathology and applied neurobiology.

[25]  R. Low,et al.  Changes in skeletal-muscle myosin isoenzymes with hypertrophy and exercise. , 1986, The Biochemical journal.

[26]  N. Curtin,et al.  Energetic aspects of muscle contraction. , 1985, Monographs of the Physiological Society.

[27]  K. Moore,et al.  X chromosome-linked muscular dystrophy (mdx) in the mouse. , 1984, Proceedings of the National Academy of Sciences of the United States of America.

[28]  R. Roy,et al.  Biochemical properties of overloaded fast-twitch skeletal muscle. , 1982, Journal of applied physiology: respiratory, environmental and exercise physiology.