Cystic Fibrosis Airway Epithelia Fail to Kill Bacteria Because of Abnormal Airway Surface Fluid
暂无分享,去创建一个
[1] J. Goldberg,et al. Role of Mutant CFTR in Hypersusceptibility of Cystic Fibrosis Patients to Lung Infections , 1996, Science.
[2] J. Wine. Cystic Fibrosis: How do CFTR mutations cause cystic fibrosis? , 1995, Current Biology.
[3] J. Pilewski,et al. How do cystic fibrosis transmembrane conductance regulator mutations produce lung disease? , 1995, Current opinion in pulmonary medicine.
[4] T. Ganz,et al. Defensins and other endogenous peptide antibiotics of vertebrates , 1995, Journal of leukocyte biology.
[5] M. Weinberger,et al. The relationship between infection and inflammation in the early stages of lung disease from cystic fibrosis , 1995, Pediatric pulmonology.
[6] P. Thorne,et al. Bioaerosol Concentrations in Noncomplaint, Complaint, and Intervention Homes in the Midwest , 1995 .
[7] D. Riches,et al. Early pulmonary inflammation in infants with cystic fibrosis. , 1995, American journal of respiratory and critical care medicine.
[8] A. Prince,et al. Cystic fibrosis epithelial cells have a receptor for pathogenic bacteria on their apical surface. , 1995, Proceedings of the National Academy of Sciences of the United States of America.
[9] F. Ognibene,et al. Tumor necrosis factor-alpha induces mucin hypersecretion and MUC-2 gene expression by human airway epithelial cells. , 1995, American journal of respiratory cell and molecular biology.
[10] D. Bailey,et al. Mucociliary clearance in patients with cystic fibrosis and in normal subjects. , 1994, American journal of respiratory and critical care medicine.
[11] Alan E. Smith,et al. Correction of cAMP-stimulated fluid secretion in cystic fibrosis airway epithelia: efficiency of adenovirus-mediated gene transfer in vitro. , 1994, Human gene therapy.
[12] M. Welsh,et al. Expression of cystic fibrosis transmembrane conductance regulator in a model epithelium. , 1994, The American journal of physiology.
[13] M. Welsh,et al. Defective fluid transport by cystic fibrosis airway epithelia. , 1994, The Journal of clinical investigation.
[14] P. Quinton,et al. Elemental composition of human airway surface fluid in healthy and diseased airways. , 1993, The American review of respiratory disease.
[15] J. Widdicombe,et al. Altered fluid transport across airway epithelium in cystic fibrosis. , 1993, Science.
[16] A. Prince,et al. Pseudomonas aeruginosa pili bind to asialoGM1 which is increased on the surface of cystic fibrosis epithelial cells. , 1993, The Journal of clinical investigation.
[17] Douglas E. Jones,et al. Airway epithelial cells are the site of expression of a mammalian antimicrobial peptide gene. , 1993, Proceedings of the National Academy of Sciences of the United States of America.
[18] M. Welsh,et al. Fluid and electrolyte transport by cultured human airway epithelia. , 1993, The Journal of clinical investigation.
[19] M. Yamaya,et al. Differentiated structure and function of cultures from human tracheal epithelium. , 1992, The American journal of physiology.
[20] F. Collins,et al. Cystic fibrosis: molecular biology and therapeutic implications. , 1992, Science.
[21] M. Knowles,et al. Activation by extracellular nucleotides of chloride secretion in the airway epithelia of patients with cystic fibrosis. , 1991, The New England journal of medicine.
[22] R. Gibson,et al. Predictive value of oropharyngeal cultures for identifying lower airway bacteria in cystic fibrosis patients. , 1991, The American review of respiratory disease.
[23] S. Douglas,et al. Increased levels of interleukin-1 in bronchoalveolar washings from children with bacterial pulmonary infections. , 1990, The American review of respiratory disease.
[24] P. Quinton. Cystic fibrosis: a disease in electrolyte transport , 1990, FASEB journal : official publication of the Federation of American Societies for Experimental Biology.
[25] M. King,et al. A pilot study of aerosolized amiloride for the treatment of lung disease in cystic fibrosis. , 1990, The New England journal of medicine.
[26] B. Strandvik,et al. Increased bronchial chloride concentration in cystic fibrosis. , 1989, Scandinavian journal of clinical and laboratory investigation.
[27] A. M. Johnson. LUNG DISEASE IN CYSTIC FIBROSIS , 1983, The Lancet.
[28] R. Matthay,et al. Cystic fibrosis pseudomonas opsonins. Inhibitory nature in an in vitro phagocytic assay. , 1981, The Journal of clinical investigation.
[29] K. Pierce,et al. Pharyngeal aspiration in normal adults and patients with depressed consciousness. , 1978, The American journal of medicine.
[30] H. Levison,et al. Mucociliary transport in trachea of patients with cystic fibrosis. , 1976, Archives of disease in childhood.
[31] M. Newhouse,et al. Pulmonary mucociliary clearance in cystic fibrosis. , 1973, The New England journal of medicine.
[32] P. Quinton. Viscosity versus composition in airway pathology. , 1994, American journal of respiratory and critical care medicine.
[33] J. Shelhamer,et al. Airway inflammation and mucous hypersecretion , 1994 .
[34] P. Davis. Pathophysiology of the lung disease in cystic fibrosis , 1993 .
[35] M. Konstan,et al. Infection and inflammation of the lung in cystic fibrosis , 1993 .
[36] R I Lehrer,et al. Defensins: antimicrobial and cytotoxic peptides of mammalian cells. , 1993, Annual review of immunology.
[37] J. Riordan,et al. The cystic fibrosis transmembrane conductance regulator. , 1993, Annual review of physiology.
[38] James M. Wilson,et al. Submucosal glands are the predominant site of CFTR expression in the human bronchus , 1992, Nature Genetics.