Recurrent Perianal Paget's Disease

Changes or disruptions in the process of mandibular development can happen in the early stages of formation, and the malformations may be isolated or part of a syndrome. Hypoplasia or aplasia of the mandibular condyles indicates underdevelopment or non-development and is associated with multiple craniofacial abnormalities. Patients who experience these congenital deformities may benefit from reconstruction using total joint prostheses. In addition, orthognathic surgery may be required to treat severe respiratory syndromes and to correct dentofacial deformities to obtain functional and aesthetic results. Therefore, this paper presents a rare case of aplasia of the mandibular condyles and treatment of dentofacial deformities associated with severe obstructive sleep apnea and the reconstruction of the temporomandibular joint.

[1]  E. Dozois,et al.  Neoplasms of Anal Canal and Perianal Skin , 2011, Clinics in colon and rectal surgery.

[2]  O. Zmora,et al.  Perianal Paget's Disease , 2006, Journal of cutaneous medicine and surgery.

[3]  J. J. Chanda Extramammary Paget's disease: prognosis and relationship to internal malignancy. , 1985, Journal of the American Academy of Dermatology.

[4]  C. J. Miller,et al.  Extramammary paget's disease of perianal skin , 1949, Cancer.

[5]  S. C. Lee,et al.  Extramammary Paget's disease of the vulva. A clinicopathologic study of 13 cases. , 1977, Cancer.