Cystoid changes within astrocytic hamartomas of the retina in tuberous sclerosis.

PURPOSE The purpose of this study was to report two unusual cases of cavitations within astrocytic hamartoma, a feature that causes the tumor to appear cystic. To our knowledge, this is the first report on cavitary astrocytic hamartoma. METHODS In this observational case report, we identify two cases of cavitary astrocytic hamartoma imaged recently with spectral domain-optical coherence tomography. RESULTS In both of our patients, the cavitary portion was visible clinically as an empty cavity surrounded by translucent tissue. Optical coherence tomography examination of both cases confirmed the presence of a cavity surrounded by tumor tissue. CONCLUSION In these two patients, optical coherence tomography showed a new feature of cavitation within retinal astrocytic hamartoma.

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