Pulmonary hypertension associated with obliterative phlebitis in IgG4-related lung disease

IgG4-related disease (IgG4-RD) is a systemic fibroinflammatory disease associated with elevated serum IgG4 level and IgG4-positive plasma cell infiltration into multiple organs [1]. In 2001, Hamano et al. [2] reported that patients with autoimmune pancreatitis have high-serum IgG4 concentrations. Subsequently, IgG4-related lesions similar to those of autoimmune pancreatitis have been identified in other organs [1] including the lungs [3]. Pulmonary hypertension can be caused by obliterative phlebitis in patients with IgG4-related lung disease http://ow.ly/EEjvE

[1]  J. Stone,et al.  IgG4-related disease , 2017, Current opinion in rheumatology.

[2]  Y. Kondoh,et al.  Efficacy of Combined Therapy with Cyclosporin and Low-Dose Prednisolone in Interstitial Pneumonia Associated with Connective Tissue Disease , 2014, Respiration.

[3]  Shinji Sato,et al.  Pulmonary arterial hypertension associated with IgG4-related disease. , 2014, Internal medicine.

[4]  A. Boner,et al.  Uncommon pulmonary presentation of IgG4-related disease in a 15-year-old boy. , 2013, Chest.

[5]  Y. Kawabata,et al.  Immunoglobulin G4‐related lung disease: Clinicoradiological and pathological features , 2013, Respirology.

[6]  T. Hibi,et al.  Comprehensive diagnostic criteria for IgG4-related disease (IgG4-RD), 2011 , 2012, Modern rheumatology.

[7]  H. Sekiguchi,et al.  Pulmonary manifestations of immunoglobulin G4-related sclerosing disease , 2011, European Respiratory Journal.

[8]  K. Chida,et al.  [Bronchiolitis with IgG4-positive plasma cell infiltration in a patient with bronchial asthma]. , 2010, Nihon Kokyuki Gakkai zasshi = the journal of the Japanese Respiratory Society.

[9]  O. Matsui,et al.  IgG4-related Lung and Pleural Disease: A Clinicopathologic Study of 21 Cases , 2009, The American journal of surgical pathology.

[10]  O. Matsui,et al.  Immunoglobulin G4-related lung disease: CT findings with pathologic correlations. , 2009, Radiology.

[11]  T. Honda,et al.  Central airway stenosis in a patient with autoimmune pancreatitis , 2009, European Respiratory Journal.

[12]  K. Tobe,et al.  [A case of bronchiolitis with IgG4-positive plasma cells infiltration associated with Mikulicz's disease and autoimmune pancreatitis]. , 2009, Nihon Kokyuki Gakkai zasshi = the journal of the Japanese Respiratory Society.

[13]  T. Nikaido,et al.  High serum IgG4 concentrations in patients with sclerosing pancreatitis. , 2001, The New England journal of medicine.

[14]  M. Koss,et al.  Pulmonary veno-occlusive disease. , 1996, Current opinion in pulmonary medicine.

[15]  A. Sherrick,et al.  The radiographic findings of fibrosing mediastinitis. , 1994, Chest.

[16]  U SERAFINI,et al.  [Bronchial asthma]. , 1950, Rassegna giuliana di medicina.