Pulmonary Aplasia: A Case Report

Developmental malformations of the lung are common but aplasia of the lung is extremely rare and usually the patients presented in early childhood with recurrent lower respiratory tract infection and respiratory distress. A 2 years and 6 months old girl presented with complaints of respiratory distress since birth and recurrent episode of cough since six month of age ,with opacity of the right hemithorax on X-ray, CT scans shows aplasia of the right lung. Patient was managed conservatively and his parents were counseled about the anomaly. The child is doing well and is in a regular follow-up with us. Aplasia of the lung should be suspected in children with recurrent respiratory distress with opacity of the hemithorax on X-ray and herniation of the opposite lung across the mediastinum. TAJ 2019; 32(1): 82-85

[1]  K. Mizushige,et al.  Right pulmonary agenesis in an elderly woman complicated by transient ischemic attack. , 2011, Internal medicine.

[2]  M. Atiq,et al.  Pulmonary agenesis--vascular airway compression and gastroesophageal reflux influence outcome. , 2006, Journal of pediatric surgery.

[3]  A. Bush,et al.  Congenital malformations of the lower respiratory tract. , 2006 .

[4]  S. Thonell.  Pediatric Chest Imaging: Chest Imaging in Infants and Children , 2004 .

[5]  C. V. Lysak,et al.  Aplasia of the right lung in a 4-year-old child: surgical stabilization of the mediastinum by diaphragm translocation leading to complete recovery from respiratory distress syndrome. , 2000, Journal of pediatric surgery.

[6]  M. Meier.  [Agenesis of the left lung in combination with a persistent left superior vena cava and al cor triatriatum sinister in a 77 year old man]. , 2000, Pneumologie.

[7]  R. Bhagat,et al.  Pulmonary aplasia: a CT appearance. , 1992, Indian pediatrics.

[8]  W. Hecker,et al.  Deviated trachea in hypoplasia and aplasia of the right lung: airway obstruction and its release by aortopexy. , 1990, Journal of pediatric surgery.

[9]  U. Dilmen,et al.  Agenesis of the lung. , 1989, The European respiratory journal.

[10]  G. Sethi,et al.  Pulmonary agenesis. , 1988, Indian Pediatrics.

[11]  D. Mendelson,et al.  Hypoplasia of the lung: CT appearance. , 1986, The Mount Sinai journal of medicine, New York.

[12]  K. M. Mohamed,et al.  Agenesis of the Lung: Report of Four Patients with Unusual Anomalies , 1985 .

[13]  W. Nyhan,et al.  Agenesis of the lung. Report of four patients with unusual anomalies. , 1985, Chest.

[14]  N. Carpenter,et al.  Agenesis of the lung associated with a chromosome abnormality (46,XX,2p+). , 1980, Journal of medical genetics.

[15]  N. Carpenter,et al.  Agenesis of the lung associated with a chromosome abnormality ( 46 , XX , 2 p + ) SUMMARY , 2022 .