Diffuse pulmonary arteriovenous malformation in a child with polysplenia syndrome.

Pulmonary arteriovenous malformation (PAVM) is usually seen as a well-circumscribed cystic mass. In this communication we describe a diffuse arteriovenous malformation in a 5-month-old infant. The lesion was seen only at the microscopic level and was associated with abdominal heterotaxy, atrial situs solitus, polysplenia, interrupted inferior vena cava, atrial septal defect, and atrioventricular canal. This uncommon association may be within the spectrum of polysplenia syndrome.

[1]  A. Bush,et al.  Multiple pulmonary arteriovenous fistulas in childhood. , 1989, International journal of cardiology.

[2]  T. Raffin,et al.  Pulmonary arteriovenous malformations: a critical update. , 1986, The American review of respiratory disease.

[3]  A. Churg,et al.  Pulmonary capillary hemangiomatosis. , 1985, The American review of respiratory disease.

[4]  B. Landing.  Five syndromes (malformation complexes) of pulmonary symmetry, congenital heart disease, and multiple spleens. , 1984, Pediatric pathology.

[5]  F. Maritz,et al.  Pulmonary arteriovenous fistulas: a case presentation and review of the literature. , 1980, South African medical journal = Suid-Afrikaanse tydskrif vir geneeskunde.

[6]  J. Spijker,et al.  Capillary haemangiomatosis of the lungs , 1978, Histopathology.

[7]  F. Brandrup,et al.  PULMONARY ARTERIOVENOUS FISTULAS IN CHILDREN A Review with Special Reference to the Disperse Telangiectatic Type, Illustrated by Report of a Case , 1973, Acta paediatrica Scandinavica.

[8]  R. Sapru,et al.  Pulmonary hypertension in patients with pulmonary arteriovenous fistulae. , 1969, British heart journal.

[9]  J. Waldhausen,et al.  PULMONARY ARTERIOVENOUS FISTULAS IN CHILDREN. , 1963, Annals of surgery.

[10]  Bosher Lh,et al.  An analysis of the pathologic anatomy of pulmonary arteriovenous aneurysms with particular reference to the applicability of local excision. , 1959 .

[11]  R. Bates,et al.  Pulmonary arteriovenous fistula. , 1955, American journal of surgery.

[12]  D. Cooley,et al.  Pulmonary telangiectasia: report of case proved by pulmonary biopsy. , 1954, The Journal of thoracic surgery.