Congenital Short QT Syndrome and Implantable Cardioverter Defibrillator Treatment:

Introduction: A congenital short QT interval constitutes a new primary electrical abnormality associated with syncope and/or sudden cardiac death. We report on the initial use of implantable cardioverter defibrillator (ICD) therapy in patients with inherited short QT interval and discuss sensing abnormalities and detection issues.

[1]  B. Lüderitz,et al.  Quality of life and driving in recipients of the implantable cardioverter-defibrillator. , 1996, The American journal of cardiology.

[2]  Y. Aizawa,et al.  Inappropriate discharges from an intravenous implantable cardioverter defibrillator due to T-wave oversensing. , 2001, Japanese circulation journal.

[3]  Martin Borggrefe,et al.  Short QT Syndrome: A Familial Cause of Sudden Death , 2003, Circulation.

[4]  I. Préda,et al.  QT Dependent T Wave Sensing , 1998, Pacing and clinical electrophysiology : PACE.

[5]  M. Bahner,et al.  Ventricular Oversensing: , 2003, Pacing and clinical electrophysiology : PACE.

[6]  J. Brugada,et al.  Right bundle branch block, persistent ST segment elevation and sudden cardiac death: a distinct clinical and electrocardiographic syndrome. A multicenter report. , 1992, Journal of the American College of Cardiology.

[7]  Y. Aizawa,et al.  Inappropriate discharges by fourth generation implantable cardioverter defibrillators in patients with ventricular arrhythmias. , 2001, Japanese circulation journal.

[8]  P. Coumel.  Catecholamine-induced severe ventricular arrhythmias with Adams-Stokes syndrome in children : report of four cases , 1978 .

[9]  S. Pinski,et al.  The proarrhythmic potential of implantable cardioverter-defibrillators. , 1995, Circulation.

[10]  G. Breithardt,et al.  [Inadequate therapies with implantable cardioverter-defibrillators--incidence, etiology, predictive factors and preventive strategies]. , 1996, Zeitschrift für Kardiologie.

[11]  M. Davies,et al.  Spectrum of clinicopathologic manifestations of arrhythmogenic right ventricular cardiomyopathy/dysplasia: a multicenter study. , 1997, Journal of the American College of Cardiology.

[12]  Judy Powell,et al.  Quality of Life in the Antiarrhythmics Versus Implantable Defibrillators Trial: Impact of Therapy and Influence of Adverse Symptoms and Defibrillator Shocks , 2002, Circulation.

[13]  E. Kosar,et al.  Problems in Managing Patients with Long QT Syndrome and Implantable Cardioverter Defibrillators: A Report of Two Cases , 1996, Pacing and clinical electrophysiology : PACE.

[14]  J. Brugada,et al.  Idiopathic Short QT Interval:A New Clinical Syndrome? , 2001, Cardiology.

[15]  Peter J. Schwartz,et al.  Diagnostic Criteria for the Long QT Syndrome An Update , 1993, Circulation.