Malonyl coenzyme a decarboxylase deficiency

[1]  G. Soltész,et al.  Dichloroacetate in the treatment of congenital lactic acidosis , 1984, Journal of Inherited Metabolic Disease.

[2]  R. Chalmers,et al.  Disorders of propionate and methylmalonate metabolism , 1982 .

[3]  J. Leonard.  Problems in the congenital lactic acidoses. , 1982, Ciba Foundation symposium.

[4]  T. Russell,et al.  Increase in fatty acid synthetase content of 3T3-L cells undergoing spontaneous and chemically induced differentiation to adipocytes. , 1979, The Biochemical journal.

[5]  J. Saudubray,et al.  Dichloroacetate as treatment for congenital lactic acidosis. , 1978, The New England journal of medicine.

[6]  P. Kolattukudy,et al.  Malonyl-CoA decarboxylase from the mammary gland of lactating rat. Purification, properties and subcellular localization. , 1978, Biochimica et biophysica acta.

[7]  P. Kolattukudy,et al.  Purification and properties of malonyl-CoA decarboxylase from rat liver mitochondria and its immunological comparison with the enzymes from rat brain, heart, and mammary gland. , 1978, Archives of biochemistry and biophysics.

[8]  T. Chen,et al.  In situ detection of mycoplasma contamination in cell cultures by fluorescent Hoechst 33258 stain. , 1977, Experimental cell research.

[9]  M. Mahoney,et al.  Studies of Methylmalonyl Coenzyme A Carbonylmutase Activity in Methylmalonic Acidemia. I. Correlation of Clinical, Hepatic, and Fibroblast Data , 1975, Pediatric Research.

[10]  P. J. Randle,et al.  Mechanism of activation of pyruvate dehydrogenase by dichloroacetate and other halogenated carboxylic acids. , 1974, The Biochemical journal.

[11]  A. Koeppen,et al.  Malonate metabolism in rat brain mitochondria. , 1974, Biochemistry.

[12]  P. Zuurendonk,et al.  Rapid separation of particulate components and soluble cytoplasm of isolated rat-liver cells. , 1974, Biochimica et biophysica acta.

[13]  A. J. Giorgio,et al.  A direct radioassay of methylmalonyl-coenzyme A mutase using enzymatically synthesized DL-(3- 14 C)methylmalonyl-CoA. , 1973, Analytical biochemistry.

[14]  J. Brodie,et al.  Cleavage of coenzyme B 12 by methylmalonyl coenzyme A mutase. , 1973, The Journal of biological chemistry.

[15]  R. Fox.  A simple incubation flask for 14CO2 collection. , 1971, Analytical biochemistry.

[16]  G. Gnoni,et al.  Properties of malonyl-CoA decarboxylase and its relation with malonyl-CoA incorporation into fatty acids by rat liver mitochondria. , 1971, European journal of biochemistry.

[17]  R. Stjernholm,et al.  Differentiation of normal and leukemic leukocytes into three groups by propionate metabolism. , 1970, Journal of the Reticuloendothelial Society.

[18]  H. Scholte.  The intracellular and intramitochondrial distribution of malonyl-CoA decarboxylase and propionyl-CoA carboxylase in rat liver. , 1969, Biochimica et biophysica acta.

[19]  W. C. Hülsmann.  On the synthesis of malonyl-coenzyme A in rabbit-heart sarcosomes , 1966 .

[20]  S. Wakil,et al.  Studies on the mechanism of fatty acid synthesis. 9. The conversion of malonyl coenzyme A to long chain fatty acids. , 1961 .

[21]  M. Lane,et al.  Further studies on mitochondrial propionyl carboxylase. , 1960, The Journal of biological chemistry.

[22]  O. H. Lowry,et al.  Protein measurement with the Folin phenol reagent. , 1951, The Journal of biological chemistry.

[23]  H. Krebs,et al.  Untersuchungen uber die Harnstoffbildung im Tierkörper , 1932 .