The Natural History of the Progression of Atrophy Secondary to Stargardt Disease (ProgStar) Studies: Design and Baseline Characteristics: ProgStar Report No. 1.

[1]  S. Sadda,et al.  COMPARISON OF MANUAL AND SEMIAUTOMATED FUNDUS AUTOFLUORESCENCE ANALYSIS OF MACULAR ATROPHY IN STARGARDT DISEASE PHENOTYPE , 2016, Retina.

[2]  R. Weleber,et al.  INSIGHTS INTO AUTOSOMAL DOMINANT STARGARDT-LIKE MACULAR DYSTROPHY THROUGH MULTIMODALITY DIAGNOSTIC IMAGING , 2016, Retina.

[3]  Hendrik P N Scholl,et al.  Assessment of estimated retinal atrophy progression in Stargardt macular dystrophy using spectral-domain optical coherence tomography , 2015, British Journal of Ophthalmology.

[4]  A. Cideciyan,et al.  Predicting Progression of ABCA4-Associated Retinal Degenerations Based on Longitudinal Measurements of the Leading Disease Front. , 2015, Investigative ophthalmology & visual science.

[5]  B. J. Klevering,et al.  Early-onset stargardt disease: phenotypic and genotypic characteristics. , 2015, Ophthalmology.

[6]  W. Hauswirth,et al.  Advancing therapeutic strategies for inherited retinal degeneration: recommendations from the Monaciano Symposium. , 2015, Investigative ophthalmology & visual science.

[7]  K. Tsubota,et al.  Clinical and Molecular Characteristics of Childhood-Onset Stargardt Disease , 2014, Ophthalmology.

[8]  Michael Bach,et al.  ISCEV Standard for full-field clinical electroretinography (2015 update) , 2014, Documenta Ophthalmologica.

[9]  P. Melillo,et al.  Macular function and morphologic features in juvenile stargardt disease: longitudinal study. , 2014, Ophthalmology.

[10]  S. Sadda,et al.  Proposed lexicon for anatomic landmarks in normal posterior segment spectral-domain optical coherence tomography: the IN•OCT consensus. , 2014, Ophthalmology.

[11]  E. Traboulsi,et al.  Predictors of visual acuity and genotype-phenotype correlates in a cohort of patients with Stargardt disease , 2014, British Journal of Ophthalmology.

[12]  K. Tsubota,et al.  A longitudinal study of Stargardt disease: quantitative assessment of fundus autofluorescence, progression, and genotype correlations. , 2013, Investigative ophthalmology & visual science.

[13]  A. Roorda,et al.  Visual Psychophysics and Physiological Optics Relationship Between Foveal Cone Structure and Clinical Measures of Visual Function in Patients With Inherited Retinal Degenerations , 2013 .

[14]  K. Tsubota,et al.  A longitudinal study of stargardt disease: clinical and electrophysiologic assessment, progression, and genotype correlations. , 2013, American journal of ophthalmology.

[15]  Amitha Domalpally,et al.  The Age-Related Eye Disease Study 2 (AREDS2): study design and baseline characteristics (AREDS2 report number 1). , 2012, Ophthalmology.

[16]  Aziz A. Khanifar,et al.  COMPARISON OF COLOR FUNDUS PHOTOGRAPHS AND FUNDUS AUTOFLUORESCENCE IMAGES IN MEASURING GEOGRAPHIC ATROPHY AREA , 2012, Retina.

[17]  A. Kampik,et al.  Enzymatic vitreolysis with ocriplasmin for vitreomacular traction and macular holes. , 2012, The New England journal of medicine.

[18]  Noemi Lois,et al.  Progression of retinal pigment epithelial atrophy in stargardt disease. , 2012, American journal of ophthalmology.

[19]  Kazunori Yamamoto,et al.  The bisretinoids of retinal pigment epithelium , 2012, Progress in Retinal and Eye Research.

[20]  T. Aleman,et al.  Macular function in macular degenerations: repeatability of microperimetry as a potential outcome measure for ABCA4-associated retinopathy trials. , 2012, Investigative ophthalmology & visual science.

[21]  R. T. Smith,et al.  Familial discordance in Stargardt disease , 2012, Molecular vision.

[22]  V. Greenstein,et al.  Transition zones between healthy and diseased retina in choroideremia (CHM) and Stargardt disease (STGD) as compared to retinitis pigmentosa (RP). , 2011, Investigative ophthalmology & visual science.

[23]  R. T. Smith,et al.  Quantitative measurements of autofluorescence with the scanning laser ophthalmoscope. , 2011, Investigative ophthalmology & visual science.

[24]  David J Lee,et al.  Effects of smoking on ocular health , 2011, Current opinion in ophthalmology.

[25]  F. Ferris,et al.  Treatment of geographic atrophy by the topical administration of OT-551: results of a phase II clinical trial. , 2010, Investigative ophthalmology & visual science.

[26]  Larry D Hubbard,et al.  Evaluation of the age-related eye disease study clinical lens grading system AREDS report No. 31. , 2010, Ophthalmology.

[27]  M. Gorin,et al.  Analysis of autofluorescent retinal images and measurement of atrophic lesion growth in Stargardt disease. , 2010, Experimental eye research.

[28]  Robert Finger,et al.  Structure-Function Correlation of the Human Central Retina , 2010, PloS one.

[29]  Scott W Cousins,et al.  Fundus autofluorescence imaging in age-related macular degeneration and geographic atrophy. , 2010, Advances in experimental medicine and biology.

[30]  Donald C Hood,et al.  A comparison of fundus autofluorescence and retinal structure in patients with Stargardt disease. , 2009, Investigative ophthalmology & visual science.

[31]  A. J. Roman,et al.  ABCA4 disease progression and a proposed strategy for gene therapy. , 2009, Human molecular genetics.

[32]  F. Ferris,et al.  Report from the NEI/FDA Ophthalmic Clinical Trial Design and Endpoints Symposium. , 2008, Investigative ophthalmology & visual science.

[33]  N. Bressler,et al.  Visual acuity as an outcome measure in clinical trials of retinal diseases. , 2007, Ophthalmology.

[34]  T. Aleman,et al.  Reduced-illuminance autofluorescence imaging in ABCA4-associated retinal degenerations. , 2007, Journal of the Optical Society of America. A, Optics, image science, and vision.

[35]  Eyal Margalit,et al.  The long-term natural history of geographic atrophy from age-related macular degeneration: enlargement of atrophy and implications for interventional clinical trials. , 2007, Ophthalmology.

[36]  Jens Dreyhaupt,et al.  Correlation between the area of increased autofluorescence surrounding geographic atrophy and disease progression in patients with AMD. , 2006, Investigative ophthalmology & visual science.

[37]  L. Dandona,et al.  Revision of visual impairment definitions in the International Statistical Classification of Diseases , 2006, BMC medicine.

[38]  A. V. Cideciyan,et al.  OUTCOME MEASURES AND THEIR APPLICATION IN CLINICAL TRIALS FOR RETINAL DEGENERATIVE DISEASES: Outline, Review, and Perspective , 2005, Retina.

[39]  U. Mansmann,et al.  Automated analysis of digital fundus autofluorescence images of geographic atrophy in advanced age-related macular degeneration using confocal scanning laser ophthalmoscopy (cSLO) , 2005, BMC ophthalmology.

[40]  Alexander Sumaroka,et al.  In vivo dynamics of retinal injury and repair in the rhodopsin mutant dog model of human retinitis pigmentosa. , 2005, Proceedings of the National Academy of Sciences of the United States of America.

[41]  Dr. K. Stargardt Über familiäre, progressive Degeneration in der Maculagegend des Auges , 1909, Albrecht von Graefes Archiv für Ophthalmologie.

[42]  Robert J. Anderson,et al.  Visual acuity loss and clinical observations in a large series of patients with Stargardt disease. , 2003, Ophthalmology.

[43]  C Bellman,et al.  Fundus autofluorescence and development of geographic atrophy in age-related macular degeneration. , 2001, Investigative ophthalmology & visual science.

[44]  J. Lupski,et al.  A photoreceptor cell-specific ATP-binding transporter gene (ABCR) is mutated in recessive Starqardt macular dystrophy , 1997, Nature Genetics.

[45]  A. Milam,et al.  Histopathology and immunocytochemistry of the neurosensory retina in fundus flavimaculatus. , 1994, Ophthalmology.

[46]  Early Treatment Diabetic Retinopathy Study design and baseline patient characteristics. ETDRS report number 7. , 1991, Ophthalmology.

[47]  G. Fishman,et al.  Visual acuity loss in patients with Stargardt's macular dystrophy. , 1987, Ophthalmology.

[48]  R. Eagle,et al.  Retinal Pigment Epithelial Abnormalities in Fundus Flavimmaculatus , 1980 .

[49]  R. Eagle,et al.  Retinal pigment epithelial abnormalities in fundus flavimaculatus: a light and electron microscopic study. , 1980, Ophthalmology.