Alveolar surfactant homeostasis and the pathogenesis of pulmonary disease.
暂无分享,去创建一个
[1] G. Dranoff,et al. Surfactant metabolism in transgenic mice after granulocyte macrophage-colony stimulating factor ablation. , 1996, The American journal of physiology.
[2] M. Papale,et al. Pulmonary alveolar microlithiasis: report on 576 cases published in the literature. , 2004, Sarcoidosis, vasculitis, and diffuse lung diseases : official journal of WASOG.
[3] J. Whitsett,et al. Adenovirus-mediated granulocyte-macrophage colony-stimulating factor improves lung pathology of pulmonary alveolar proteinosis in granulocyte-macrophage colony-stimulating factor-deficient mice. , 1998, Human gene therapy.
[4] R. Nishinakamura,et al. Persistence of pulmonary pathology and abnormal lung function in IL-3/GM-CSF/IL-5 β c receptor-deficient mice despite correction of alveolar proteinosis after BMT , 1997, Bone Marrow Transplantation.
[5] P. Sly,et al. Altered stability of pulmonary surfactant in SP-C-deficient mice , 2001, Proceedings of the National Academy of Sciences of the United States of America.
[6] A. Jobe,et al. Surfactant metabolism in SP-D gene-targeted mice. , 2000, American journal of physiology. Lung cellular and molecular physiology.
[7] S. Altın,et al. Mutations in SLC34A2 cause pulmonary alveolar microlithiasis and are possibly associated with testicular microlithiasis. , 2006, American journal of human genetics.
[8] J. Whitsett,et al. Allelic heterogeneity in hereditary surfactant protein B (SP-B) deficiency. , 2000, American journal of respiratory and critical care medicine.
[9] Chao Xing,et al. Adult-onset pulmonary fibrosis caused by mutations in telomerase , 2007, Proceedings of the National Academy of Sciences.
[10] W. Lu,et al. Aerosolized GM-CSF ameliorates pulmonary alveolar proteinosis in GM-CSF-deficient mice. , 1999, American journal of physiology. Lung cellular and molecular physiology.
[11] Jeffrey L. Brodsky,et al. One step at a time: endoplasmic reticulum-associated degradation , 2008, Nature Reviews Molecular Cell Biology.
[12] S. Harari,et al. Update on diffuse parenchymal lung disease , 2010, European Respiratory Review.
[13] R. Lynch,et al. Image acquisition for colocalization using optical microscopy. , 2008, American journal of physiology. Cell physiology.
[14] N. Cheong,et al. Functional and Trafficking Defects in ATP Binding Cassette A3 Mutants Associated with Respiratory Distress Syndrome* , 2006, Journal of Biological Chemistry.
[15] H. Wong,et al. Adaptation and increased susceptibility to infection associated with constitutive expression of misfolded SP-C , 2006, The Journal of cell biology.
[16] S. Cheung,et al. Brief Definitive Report , 2022 .
[17] S. Russo,et al. Deletion of exon 4 from human surfactant protein C results in aggresome formation and generation of a dominant negative , 2003, Journal of Cell Science.
[18] Peter F. Crossno,et al. Endoplasmic reticulum stress in alveolar epithelial cells is prominent in IPF: association with altered surfactant protein processing and herpesvirus infection. , 2008, American journal of physiology. Lung cellular and molecular physiology.
[19] W. Travis,et al. Diffuse lung disease in young children: application of a novel classification scheme. , 2007, American journal of respiratory and critical care medicine.
[20] G. Holcomb. Lung transplantation for treatment of infants with surfactant protein B deficiency , 1998 .
[21] Susan E. Wert,et al. Surfactant Protein-D Regulates Surfactant Phospholipid Homeostasis in Vivo * , 1998, The Journal of Biological Chemistry.
[22] B. Kaissling,et al. Expression of type II NaPi cotransporter in alveolar type II cells , 1999 .
[23] J. Pérez-Gil,et al. Structure of pulmonary surfactant membranes and films: the role of proteins and lipid-protein interactions. , 2008, Biochimica et biophysica acta.
[24] H. Colten,et al. A mutation in the surfactant protein B gene responsible for fatal neonatal respiratory disease in multiple kindreds. , 1994, The Journal of clinical investigation.
[25] G. Dranoff,et al. Involvement of granulocyte-macrophage colony-stimulating factor in pulmonary homeostasis. , 1994, Science.
[26] C. Ruppert,et al. Epithelial endoplasmic reticulum stress and apoptosis in sporadic idiopathic pulmonary fibrosis. , 2008, American journal of respiratory and critical care medicine.
[27] J. Whitsett,et al. Surfactant protein D influences surfactant ultrastructure and uptake by alveolar type II cells. , 2005, American journal of physiology. Lung cellular and molecular physiology.
[28] H. Sugimura,et al. Isolation and localization of type IIb Na/Pi cotransporter in the developing rat lung. , 2000, The American journal of pathology.
[29] J. Krischer,et al. Characteristics of a large cohort of patients with autoimmune pulmonary alveolar proteinosis in Japan. , 2008, American journal of respiratory and critical care medicine.
[30] A. Fisher,et al. Identification of LBM180, a Lamellar Body Limiting Membrane Protein of Alveolar Type II Cells, as the ABC Transporter Protein ABCA3* , 2002, The Journal of Biological Chemistry.
[31] J. Whitsett,et al. In defense of the lung: surfactant protein A and surfactant protein D. , 2006, Current opinion in pharmacology.
[32] J. Johansson,et al. Mutations linked to interstitial lung disease can abrogate anti-amyloid function of prosurfactant protein C. , 2008, The Biochemical journal.
[33] A. Dunn,et al. Granulocyte/macrophage colony-stimulating factor-deficient mice show no major perturbation of hematopoiesis but develop a characteristic pulmonary pathology. , 1994, Proceedings of the National Academy of Sciences of the United States of America.
[34] N. Grishin,et al. Genetic defects in surfactant protein A2 are associated with pulmonary fibrosis and lung cancer. , 2009, American journal of human genetics.
[35] G. Raghu,et al. Telomere shortening in familial and sporadic pulmonary fibrosis. , 2008, American journal of respiratory and critical care medicine.
[36] J. Whitsett,et al. ABCA3 gene mutations in newborns with fatal surfactant deficiency. , 2004, The New England journal of medicine.
[37] R. Chibbar,et al. Nonspecific interstitial pneumonia and usual interstitial pneumonia with mutation in surfactant protein C in familial pulmonary fibrosis , 2004, Modern Pathology.
[38] M. Dishop,et al. A Protocol for the Handling of Tissue Obtained by Operative Lung Biopsy: Recommendations of the chILD Pathology Co-Operative Group , 2006, Pediatric and developmental pathology : the official journal of the Society for Pediatric Pathology and the Paediatric Pathology Society.
[39] U. Dirksen,et al. Human pulmonary alveolar proteinosis associated with a defect in GM-CSF/IL-3/IL-5 receptor common beta chain expression. , 1997, The Journal of clinical investigation.
[40] J. Whitsett,et al. Hydrophobic surfactant proteins in lung function and disease. , 2002, The New England journal of medicine.
[41] Leslie A. Smith,et al. The hyperbilirubinemic Gunn rat is resistant to the pressor effects of angiotensin II. , 2005, American journal of physiology. Renal physiology.
[42] C. Galambos. Clinical, radiological and pathological features of ABCA3 mutations in children , 2009 .
[43] Huqun,et al. Mutations in the SLC34A2 gene are associated with pulmonary alveolar microlithiasis. , 2007, American journal of respiratory and critical care medicine.
[44] A. Hamvas,et al. Lung Transplantation for Inherited Disorders of Surfactant Metabolism , 2008 .
[45] B. Stripp,et al. Targeted disruption of the surfactant protein B gene disrupts surfactant homeostasis, causing respiratory failure in newborn mice. , 1995, Proceedings of the National Academy of Sciences of the United States of America.
[46] J. Behr,et al. Update in diffuse parenchymal lung disease 2008. , 2009, American journal of respiratory and critical care medicine.
[47] L. Nogee. Alterations in SP-B and SP-C expression in neonatal lung disease. , 2004, Annual review of physiology.
[48] J. Whitsett,et al. Expression of ABCA3 in Developing Lung and Other Tissues , 2007, The journal of histochemistry and cytochemistry : official journal of the Histochemistry Society.
[49] H. Colten,et al. Population-Based Estimates of Surfactant Protein B Deficiency , 2000, Pediatrics.
[50] J. Whitsett,et al. GM-CSF regulates alveolar macrophage differentiation and innate immunity in the lung through PU.1. , 2001, Immunity.
[51] B. Stripp,et al. Altered surfactant function and structure in SP-A gene targeted mice. , 1996, Proceedings of the National Academy of Sciences of the United States of America.
[52] F. Askin,et al. A mutation in the surfactant protein C gene associated with familial interstitial lung disease. , 2001, The New England journal of medicine.
[53] Jeffrey R. Galvin,et al. From the archives of the AFIP: pulmonary alveolar proteinosis. , 2008, Radiographics : a review publication of the Radiological Society of North America, Inc.
[54] J. Wright. Immunoregulatory functions of surfactant proteins , 2005, Nature Reviews Immunology.
[55] J. Seymour,et al. Pulmonary alveolar proteinosis: progress in the first 44 years. , 2002, American journal of respiratory and critical care medicine.
[56] Jeffrey L Brodsky,et al. The Recognition and Retrotranslocation of Misfolded Proteins from the Endoplasmic Reticulum , 2008, Traffic.
[57] S. Wert,et al. Inherited Surfactant Disorders , 2008 .
[58] P. Lansdorp,et al. Telomerase mutations in families with idiopathic pulmonary fibrosis. , 2007, The New England journal of medicine.
[59] A. Jobe,et al. Characteristics of surfactant from SP-A-deficient mice. , 1998, American journal of physiology. Lung cellular and molecular physiology.
[60] J. A. Maguire,et al. Misfolded BRICHOS SP-C mutant proteins induce apoptosis via caspase-4- and cytochrome c-related mechanisms. , 2007, American journal of physiology. Lung cellular and molecular physiology.
[61] Huqun,et al. A case of pulmonary alveolar microlithiasis with an intragenetic deletion in SLC34A2 detected by a genome-wide SNP study , 2009, Thorax.
[62] N. Müller,et al. Metabolic lung disease: imaging and histopathologic findings. , 2005, European journal of radiology.
[63] J. Whitsett,et al. ABCA3 mutations associated with pediatric interstitial lung disease. , 2005, American journal of respiratory and critical care medicine.
[64] B. Rubin,et al. Familial pulmonary alveolar proteinosis caused by mutations in CSF2RA , 2008, The Journal of experimental medicine.
[65] K. Traczyk,et al. [Pulmonary alveolar proteinosis]. , 1961, Gruzlica.
[66] C. Begley,et al. Hematopoietic and lung abnormalities in mice with a null mutation of the common beta subunit of the receptors for granulocyte-macrophage colony-stimulating factor and interleukins 3 and 5. , 1995, Proceedings of the National Academy of Sciences of the United States of America.
[67] B. Kaissling,et al. Expression of type II Na-Picotransporter in alveolar type II cells. , 1999, American journal of physiology. Lung cellular and molecular physiology.
[68] G. Laurent,et al. Adult familial cryptogenic fibrosing alveolitis in the United Kingdom , 2000, Thorax.
[69] Jonathan Haines,et al. Heterozygosity for a surfactant protein C gene mutation associated with usual interstitial pneumonitis and cellular nonspecific interstitial pneumonitis in one kindred. , 2002, American journal of respiratory and critical care medicine.
[70] A. Hamvas,et al. Surfactant Composition and Function in Patients with ABCA3 Mutations , 2006, Pediatric Research.
[71] B. Trapnell,et al. GM-CSF autoantibodies and neutrophil dysfunction in pulmonary alveolar proteinosis. , 2007, The New England journal of medicine.
[72] Susan E Wert,et al. Expression of a Human Surfactant Protein C Mutation Associated with Interstitial Lung Disease Disrupts Lung Development in Transgenic Mice* , 2003, Journal of Biological Chemistry.