Auditory Functions In Oto-Palato-Digital Syndrome

The oto-palato-digital (OPD) syndrome is a rare X linked disorder characterized by generalized skeletal dysplasia. A case with major features of mild conductive hearing loss, with hyperteleorism, cleft soft palate, hand and foot abnormalities is presented. The evaluation of the auditory functions of case was performed by objective and subjective hearing tests with radiological findings of temporal bone. Hearing aids were prescribed for both ears for the mild conductive hearing loss. The patient remained in good health for three years.

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