Craniofacial Fibrous Dysplasia of Orbit

Fibrous dysplasia is a benign, rare, and idiopathic skeletal disorder characterized by replacement and expansion of medullary bone by disorganized fibro-osseous tissue. Treatment for these lesions is usually sought for cosmetic or functional reasons. The surgical approaches vary from watchful expectancy for the lesion to stop growing after puberty to conservative resection to radical resection. In this case reports, 3 patients with craniofacial fibrous dysplasia involving orbital region underwent surgery. In these primary cases, resection and immediate reconstruction were performed to regain facial contour, dental occlusion, and masticatory function. Significant improvement was seen in facial appearance, and all patients also felt that there had been improvement aesthetically. Therefore, conservative treatment for fibrous dysplasia, unless there is involvement of vital structure as orbital region, can be suggested. Early surgery to address progressive sensory disturbance is recommended so as to avoid the hazards of late-stage decompression.

[1]  N. Güler,et al.  Cystic fibrous dysplasia in mandible , 2007 .

[2]  P. Parida,et al.  A clinicoradiologic analysis of symptomatic craniofacial fibro-osseous lesions , 2007, Otolaryngology--head and neck surgery : official journal of American Academy of Otolaryngology-Head and Neck Surgery.

[3]  F. Soares,et al.  Synchronous ameloblastoma and orthokeratinized odontogenic cyst of the mandible. , 2006, Journal of oral pathology & medicine : official publication of the International Association of Oral Pathologists and the American Academy of Oral Pathology.

[4]  V. Ugboko,et al.  Aggressive form of fibrous dysplasia of the mandible in childhood: Case report , 2006 .

[5]  B. Horswell,et al.  Craniofacial fibrous dysplasia of the fronto-orbital region: a case series and literature review. , 2001, Journal of oral and maxillofacial surgery : official journal of the American Association of Oral and Maxillofacial Surgeons.

[6]  J. Nerad,et al.  Ophthalmic manifestations of fibrous dysplasia: a disease of children and adults. , 1998, Ophthalmology.

[7]  S. Zinreich,et al.  3‐D CT for cranial facial and laryngeal surgery , 1988, The Laryngoscope.

[8]  Y. Hertzanu,et al.  Computed Tomography of Craniofacial Fibrous Dysplasia , 1984, Journal of computer assisted tomography.

[9]  I. Jackson,et al.  Treatment of cranioorbital fibrous dysplasia , 1982 .