论文信息 - Traumatic hematoma of the posterior fossa in rare coagulation disorder--case report.

Traumatic hematoma of the posterior fossa in rare coagulation disorder--case report.

A case of congenital deficiency of factor XIII (fibrin-stabilizing factor) with traumatic hematoma of the posterior fossa which was successfully treated is described. Congenital deficiency of factor XIII is a quite rare coagulation disorder and 100 or more cases with this disease have been reported. We have found a few cases undergoing craniotomy for associated intracranial hematomas. In this report, the diagnostic and therapeutic problems associated with this rare coagulation disorder are also briefly discussd.

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