Very-long-chain fatty acid metabolism in adrenoleukodystrophy protein-deficient mice

[1]  Y. Kuroiwa,et al.  Adrenoleukodystrophy: detection of increased very long chain fatty acids by high-performance liquid chromatography , 1983, Journal of Neurology.

[2]  K. Nave,et al.  Targeted inactivation of the X‐linked adrenoleukodystrophy gene in mice , 1997, Journal of neuroscience research.

[3]  D. Valle,et al.  Identification of a fourth half ABC transporter in the human peroxisomal membrane. , 1997, Human molecular genetics.

[4]  H. Moser,et al.  A mouse model for X-linked adrenoleukodystrophy. , 1997, Proceedings of the National Academy of Sciences of the United States of America.

[5]  A. Holzinger,et al.  Primary structure of human PMP69, a putative peroxisomal ABC-transporter. , 1997, Biochemical and biophysical research communications.

[6]  H. Moser,et al.  Adrenoleukodystrophy: phenotype, genetics, pathogenesis and therapy. , 1997, Brain : a journal of neurology.

[7]  T. Aoyama,et al.  Molecular Cloning of cDNA Encoding Rat Very Long-chain Acyl-CoA Synthetase* , 1996, The Journal of Biological Chemistry.

[8]  J. Mandel,et al.  A close relative of the adrenoleukodystrophy (ALD) gene codes for a peroxisomal protein with a specific expression pattern. , 1996, Proceedings of the National Academy of Sciences of the United States of America.

[9]  Takurou Kobayashi,et al.  Molecular analysis of X-linked adrenoleukodystrophy patients , 1995, Journal of the Neurological Sciences.

[10]  Y. Suzuki,et al.  Adrenoleukodystrophy: the restoration of peroxisomal beta-oxidation by transfection of normal cDNA. , 1995, Biochemical and biophysical research communications.

[11]  M. Wilcke,et al.  Novel Peroxisomal Populations in Subcellular Fractions from Rat Liver , 1995, The Journal of Biological Chemistry.

[12]  T. Iwaki,et al.  Adrenoleukodystrophy gene encodes an 80 kDa membrane protein. , 1994, Biochemical and biophysical research communications.

[13]  Jean Mosser,et al.  Putative X-linked adrenoleukodystrophy gene shares unexpected homology with ABC transporters , 1993, Nature.

[14]  C. Higgins,et al.  ABC transporters: from microorganisms to man. , 1992, Annual review of cell biology.

[15]  I. Singh,et al.  Transport of fatty acids into human and rat peroxisomes. Differential transport of palmitic and lignoceric acids and its implication to X-adrenoleukodystrophy. , 1992, The Journal of biological chemistry.

[16]  T. Hashimoto,et al.  Effects of sodium 2-[5-(4-chlorophenyl)pentyl]-oxirane-2-carboxylate (POCA) on fatty acid oxidation in fibroblasts from patients with peroxisomal diseases. , 1991, Biochemical pharmacology.

[17]  I. Singh,et al.  Topographical localization of peroxisomal acyl-CoA ligases: differential localization of palmitoyl-CoA and lignoceroyl-CoA ligases. , 1990 .

[18]  上条 桂樹.  The 70-kDa peroxisomal membrane protein is a member of the MDR (P-glycoprotein)-related ATP-binding protein superfamily , 1990 .

[19]  I. Singh,et al.  Peroxisomal lignoceroyl-CoA ligase deficiency in childhood adrenoleukodystrophy and adrenomyeloneuropathy. , 1988, Proceedings of the National Academy of Sciences of the United States of America.

[20]  N. Usuda,et al.  Purification of membrane polypeptides of rat liver peroxisomes. , 1986, Journal of biochemistry.