Hereditaryhemochromatosisisaniron-overloaddisorderresultingfrommutationsinproteinspresumedto beinvolvedinthemaintenanceofironhomeostasis.Mutationsinhemojuvelin(HJV)causesevere,early-onset juvenilehemochromatosis.ThenormalfunctionofHJVisunknown.Juvenilehemochromatosispatientshave decreasedurinaryleve

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