Acro-osteolysis with multiple resorption and retarded eruption of some permanent teeth. Report of a case.

A very rare case of acro-osteolysis with skull and teeth disorders is presented. Some teeth are absent and some unerupted. The majority of remaining teeth show different degrees of cervical resorption. There are mainly root fragments in the mandible. In spite of nonfamilial occurrence this can be regarded as a heritable disorder and classified in the group of arthro-dento-osteo dysplasia syndrome.