Aortopulmonary window with ventricular septal defect and pulmonary atresia: prenatal diagnosis and successful early surgical correction

We report a case in which aortopulmonary window (APW) in combination with pulmonary atresia was diagnosed correctly in a neonate by echocardiography. Prenatal echocardiography showed progression of tetralogy of Fallot to pulmonary atresia with retrograde pulmonary perfusion, concealing the concomitant APW in fetal life. Due to intractable heart failure, primary correction was successfully performed at the age of 4 weeks (weight 2280 g). Copyright © 2004 ISUOG. Published by John Wiley & Sons, Ltd.

[1]  M. Russo,et al.  Aortopulmonary window coexisting with tetralogy of Fallot: Echocardiographic diagnosis , 1990, Pediatric Cardiology.

[2]  M. Respondek-Liberska,et al.  Significant Fetal Pulmonary Regurgitation as a Possible Prenatal Sign of Aorto-Pulmonary Window in the Fetus with Intrauterine Growth Retardation , 2003, Fetal Diagnosis and Therapy.

[3]  P. Collinet,et al.  Prenatal Diagnosis of an Aorto-Pulmonary Window by Fetal Echocardiography , 2002, Fetal Diagnosis and Therapy.

[4]  J. Smallhorn,et al.  Images in cardiovascular medicine. Prenatal diagnosis of aortopulmonary window by fetal echocardiography. , 2002, Circulation.

[5]  C. Mavroudis,et al.  Surgical management of aortopulmonary window: a 40-year experience. , 2002, European journal of cardio-thoracic surgery : official journal of the European Association for Cardio-thoracic Surgery.

[6]  B. Marino,et al.  Aortopulmonary window coexisting with tetralogy of Fallot. , 2001, The Journal of cardiovascular surgery.

[7]  E. Malec,et al.  Surgical treatment of aortopulmonary window with tetralogy of Fallot. , 2001, Scandinavian cardiovascular journal : SCJ.

[8]  S. Colan,et al.  In utero pulmonary artery and aortic growth and potential for progression of pulmonary outflow tract obstruction in tetralogy of Fallot. , 1995, Journal of the American College of Cardiology.

[9]  J. Seward,et al.  Aortopulmonary window: factors associated with early and late success after surgical treatment. , 1993, Mayo Clinic proceedings.

[10]  M. Burch,et al.  Accuracy of cross-sectional echocardiography in diagnosis of aortopulmonary window. , 1991, The American journal of cardiology.

[11]  S. Kothari,et al.  Tetralogy of Fallot with aortopulmonary window. , 1988, International journal of cardiology.

[12]  S. Ho,et al.  Aortopulmonary septal defect coexisting with ventricular septal defect and pulmonary atresia. , 1983, The Annals of thoracic surgery.

[13]  F. Crawford,et al.  Tetralogy of Fallot with coexisting type II aortopulmonary window. , 1981, The Annals of thoracic surgery.

[14]  M. Quero,et al.  Aorticopulmonary Window Associated With Tetralogy of Fallot , 1976, Angiology.

[15]  T. Graham,et al.  Aortopulmonary window, ventricular septal defect, and membranous pulmonary atresia with a diagnosis of truncus arteriosus. , 1974, Chest.