Clear Cell Sarcoma of Ileum in an Elderly Male: A Rare Case with Review of Literature

Clear cell sarcoma (CCS) is a rare malignant tumor that was described first by Enzinger [1]. Owing to it’s clinical, pathological and morphological similarities with melanoma, it is also termed as soft tissue melanoma. Deep soft tissues of the lower extremities close to the tendon, fascia, or aponeuroses are most common sites for CCS [2]. This aggressive malignancy is preferentially seen in adolescents and young adults and is associated with a high propensity of local recurrence, regional lymph node metastases, and distant metastases [1,2]. Primary gastrointestinal tract involvement with CCS is extremely rare. Thus there is lack of information regarding optimal management of GIT CCS and evidence based treatment protocol is still elusive. We are reporting an ileal CCS with 7 months follow up.