Two-staged en bloc excision of a retinal haemangioma

A 31-year-old man presented to us with diminution of vision in the right eye which he noticed since 10 days, with a visual acuity of hand motions only. On examination, festooned pupil and a complicated cataract were noted with no view of the retina. Ultrasonography of the right eye showed retinal detachment in all quadrants with suspected areas of traction and membranes in the vitreous. Left eye examination revealed a normal anterior and posterior segment. Intraoperatively, he underwent a pars plana lensectomy following which an inferior large retinal haemangioma was noted with dilated and tortuous feeder artery and draining vein. The haemangioma was managed by a two-staged procedure including ligature of the feeder artery in the first surgery and the en bloc excision of the angioma at the time of the second procedure after significant shrinkage in size of the tumour.

[1]  G. Khurshid Transvitreal endoresection of refractory retinal capillary hemangioblastoma after feeder vessel ligation. , 2013, Ophthalmic surgery, lasers & imaging retina.

[2]  P. Rozas,et al.  Retinal capillary hemangioma and von Hippel-Lindau disease: Diagnostic and therapeutic implications , , 2011 .

[3]  R. Salazar,et al.  Hemangioma capilar retiniano y enfermedad de von Hippel-Lindau: implicaciones diagnósticas y terapéuticas , 2011 .

[4]  L. Wittenberg,et al.  Treatment of a von Hippel-Lindau retinal capillary hemangioma with photodynamic therapy. , 2008, Canadian journal of ophthalmology. Journal canadien d'ophtalmologie.

[5]  Z. Gregor,et al.  Surgical management of retinal capillary hemangioblastoma associated with retinal detachment. , 2008, Retina.

[6]  S. Michels,et al.  [Intravitreal anti-VEGF therapy for capillary hemangioblastomas in von Hippel-Lindau disease]. , 2008, Klinische Monatsblätter für Augenheilkunde.

[7]  David J. Wilson,et al.  Internal en bloc resection and genetic analysis of retinal capillary hemangioblastoma. , 2007, Archives of ophthalmology.

[8]  M. Farah,et al.  Transretinal Feeder Vessel Ligature in von Hippel-Lindau Disease , 2001, European journal of ophthalmology.

[9]  K. Mireskandari,et al.  Transpupillary thermotherapy for retinal capillary hemangioma in von Hippel-Lindau disease. , 2000, Ophthalmic surgery and lasers.

[10]  P. Rozas,et al.  [Retinal capillary hemangioma and von Hippel-Lindau disease: diagnostic and therapeutic implications]. , 2011, Archivos de la Sociedad Espanola de Oftalmologia.

[11]  S. Richard,et al.  Vitreoretinal surgery for severe retinal capillary hemangiomas in von hippel-lindau disease. , 2011, Ophthalmology.

[12]  A. Markoe,et al.  Salvage external beam radiotherapy of retinal capillary hemangiomas secondary to von Hippel-Lindau disease: visual and anatomic outcomes. , 2004, Ophthalmology.