Achilles tendon lengthening for ankle equinus deformity in hemophiliacs: 23 patients followed for 1–24 years

Background Bleeding in the calf or ankle joint may lead to ankle equinus deformity, particularly in childhood and during adolescence. We assessed the long-term functional and radiographic results after Achilles tendon lengthening for ankle equinus deformity in hemophiliacs. Patients and methods Between 1975 and 1986, 30 hemophilic patients with pes equinus were surgically managed by Achilles tendon lengthening. Of these, 23 were followed up prospectively twice a year for an average of 13 (1–24) years. The mean age at operation was 29 (12–46) years. The clinical results were documented according to the score of the Advisory Committee of the World Federation of Hemophilia (WFH), while radio-graphs were evaluated using the Pettersson score. On average, preoperative ankle equinus deformity was 21 (5–55) degrees. Mean range of motion was 21 (5–42) degrees prior to surgery. Results At the first postoperative examination 1 year after surgery, 21/23 cases were improved, and 9/21 reached dorsiflexion to at least neutral position. At the last follow-up, ankle equinus deformity was 10 (4–20) degrees on average. 20/23 patients still showed significant improvement compared to their condition before surgery. 7 patients still had complete correction of the equinus deformity, while mean range of motion decreased constantly over the observation period. The clinical score was significantly improved 1 year after surgery and diminished only slightly afterwards. Radio-graphic outcome deteriorated, with scores rising from 4.3 (1–10) points preoperatively to 7.3 (3–12) points at last follow-up. Interpretation Most patients treated for hemophilic pes equinus by Achilles tendon lengthening experienced long-term benefit concerning the equinus deformity, but gradually lost overall movement of the ankle joint. Progression of the ankle arthropathy cannot be hindered. ▪

[1]  T. Wallny,et al.  Long‐term follow‐up after osteotomy for haemophilic arthropathy of the knee , 2003, Haemophilia : the official journal of the World Federation of Hemophilia.

[2]  T. Wallny,et al.  Long‐term follow‐up after intertrochanteric varus osteotomy for haemophilic arthropathy of the hip , 2002, Haemophilia : the official journal of the World Federation of Hemophilia.

[3]  E. Rodríguez‐Merchán Therapeutic options in the management of articular contractures in haemophiliacs , 1999, Haemophilia : the official journal of the World Federation of Hemophilia.

[4]  W. Ribbans,et al.  Management of equinus contractures of the ankle in haemophilia , 1999, Haemophilia : the official journal of the World Federation of Hemophilia.

[5]  Phillips Am,et al.  Hemophilic ankle arthropathy. , 1996 .

[6]  A. M. Phillips,et al.  Hemophilic Ankle Arthropathy , 1996, Clinical orthopaedics and related research.

[7]  B. Glader,et al.  Arthropathy of the ankle in hemophilia. , 1991, The Journal of bone and joint surgery. American volume.

[8]  R. P. Johnson,et al.  Five stages of joint disintegration compared with range of motion in hemophilia. , 1985, Clinical orthopaedics and related research.

[9]  H. Pettersson,et al.  Diagnostic Imaging in Hemophilia , 1985, Springer London.

[10]  H. Pettersson,et al.  A radiologic classification of hemophilic arthropathy. , 1980, Clinical orthopaedics and related research.

[11]  Niemann Km Surgical correction of flexion deformities in hemophilia. , 1971 .

[12]  K. Niemann Surgical correction of flexion deformities in hemophilia. , 1971, The American surgeon.

[13]  R. Fauchet,et al.  [Tenotomy of the Achilles tendon for talipes equinus in a hemophiliac B]. , 1965, Hemostase.

[14]  I. Nilsson,et al.  Haemophilia in Sweden. VI. Treatment of haemophilia A with the human antihaemophilic factor preparation (fraction I--0). , 2009, Acta medica Scandinavica. Supplementum.