论文信息 - Exophthalmos, pretibial myxedema, hypertrophic osteoarthropathy (EMO)症候群の1例

Exophthalmos, pretibial myxedema, hypertrophic osteoarthropathy (EMO)症候群の1例

1967年Braun-Falcoらにより報告されたexophthalmos, pretibial myxedema, osteoarthropathy (EMO)症候群は,甲状腺機能亢進症に眼球突出,〓骨前粘液水腫,太鼓ばち指を伴うきわめてまれな病態である.われわれはpretibial myxedemaにsteroid局注の著効したEMO症候群の1例を経験した.症例は60才,女性.眼球突出を有し,甲状腺機能亢進症の治療開始10カ月後に両側下腿腫脹,太鼓ばち指が出現,下腿病変部の組織学的検索ではpretibial myxedemaの所見でありEMO症候群と診断. pretibial myxedemaに対しsteroid局注を試みたところ著効を示したが,眼球突出,太鼓ばち指には変化を認めなかった.また,本病態発生の機序について文献的考察を加えた.

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