A rare case report of Dowling- Degos disease: Reticulate acropigmentation of kitamura overlap

Dowling Degos disease (DDD) and Reticulate Acropigmentation of Kitamura (RAPK) belong to a rare group of autosomal dominant inherited reticulated pigmentary disorders. We are reporting a case of a 38 year old female patient who presented to us with multiple asymptomatic dark coloured lesions over the dorsa of the hands and feet, axilla, groin, periorbital region, front and sides of neck. There were also multiple dark comedo-like lesions, perioral pitted acneiform scars and multiple palmar pits. Based on the clinical and histopathological findings, a diagnosis of an overlap of DDD and RAPK was made. Such overlaps of features of reticulate pigmentation have been rarely mentioned in the literature.

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